Unilateral renal cystic disease in an adult

Curry, Nancy S.; Chung, Chooryung J.; Gordon, Brian

doi:10.1007/bf00198201

Cited by 20 publications

(12 citation statements)

References 16 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Since CT became popular, the surgical confirmation of URCD is no longer needed if patients have characteristic CT findings in combination with genetic and clinical manifestations. 14 Unilateral cystic change of the kidney has been reported in children as an unusual presenting manifestation of ADPKD. 15,16 and has recently been reported to occur in autosomal recessive polycystic kidney disease.…”

Section: Discussionmentioning

confidence: 99%

Unilateral renal cystic disease: a case report study

et al. 2019

View full text Add to dashboard Cite

Unilateral renal cystic disease (URCD) of kidney is a non-familial, extremely rare condition, characterized by replacement of the renal parenchyma of one kidney by a cluster of multiple cysts of varying size with a normal contralateral kidney. It is morphologically indistinguishable from autosomal dominant polycystic kidney disease (ADPKD); as such, hepatic and pancreatic cysts is not seen and shows no progressive deterioration in renal function; thus, differentiating ADPKD from URCD becomes important. We report a case of URCD documented by clinical and radiological imaging. A 21 year-old female, presented with history of mild lancinating pain in the left flank for 6 years which aggravated in the past 3 days, with no history of lower urinary tract symptoms. No significant family illnesses reported. Examination showed normal vitals and ballotability present and associated tenderness on deep palpation in left lumbar region. Laboratory findings were within normal limits. Ultrasonography of abdomen and pelvis showed left hydronephrosis with multiple cysts. CECT Abdomen revealed an enlarged left kidney (∼15×16×10 cm) filled with variable sized round, well-marginated multiple cysts. Renal ultrasound was performed on patient’s parents and her siblings and ruled out cystic renal disease. Hence, authors considered the diagnosis of URCD in this patient. In conclusion, treatment and managing guidelines of URCD have not been mentioned in any of the medical literatures. There is little information regarding the progression of URCD. Hence there is a need for further understanding of pathogenesis, progression and management of these patients.

show abstract

Section: Discussionmentioning

confidence: 99%

Unilateral renal cystic disease: a case report study

et al. 2019

View full text Add to dashboard Cite

show abstract

“…The lack of suspect lymph nodes and homogeneous tumor mass as well as the presence of cysts in other areas of the affected kidney in our patient made the diagnosis of cystic nephroma less likely. Unilateral renal cystic disease is a less well known entity reported that is non-familial and non-progressive [1,2]. Segmental multicystic dysplastic kidney disease was unlikely in our patient since on the CT scan there was normal contrast enhancement in the renal tissue adjacent to the cysts and a lack of evidence of duplication of the collecting system.…”

mentioning

confidence: 65%

Unilateral localized cystic kidney: Answer

Verghese

Kim

2010

Pediatr Nephrol

View full text Add to dashboard Cite

“…There are no associated cysts in the unaffected kidney or any other intra‐abdominal organ. Some studies have reported small simple cysts in the other kidney 3 . Others have reported the evolution of unilateral disease into bilateral disease after a long‐ term follow up 4 …”

Section: Discussionmentioning

confidence: 99%

Unilateral and segmental cystic disease of the kidney

et al. 2005

View full text Add to dashboard Cite

Unilateral and segmental cystic disease is a rare cystic disease of the kidney. Except for its unilaterality, it resembles autosomal dominant polycystic kidney disease on gross and histological examination. It also lacks genetic background and progressive deterioration of renal function. Only a small number of unilateral and segmental cystic disease of the kidney cases have been reported to date. The present case is a report of a 69-year-old man who had a large multicystic mass involving the lower and middle part of the right kidney with normal residual renal parenchyma at the upper pole. The left kidney was entirely normal. All the laboratory tests were within normal limits. Right nephrectomy was performed because of a strong suspicion of malignancy.

show abstract

Unilateral renal cystic disease in an adult

Cited by 20 publications

References 16 publications

Unilateral renal cystic disease: a case report study

Unilateral renal cystic disease: a case report study

Unilateral localized cystic kidney: Answer

Unilateral and segmental cystic disease of the kidney

Contact Info

Product

Resources

About