Unilateral Lung Agenesis in an infant with prenatal diagnosis of Congenital Lobar Emphysema

A Rare Etiology of Unilateral Pseudo-Pulmonary Fibrosis in a Puerto Rican Child

“…Typical findings on a plain chest radiographic image of unilateral pulmonary artery agenesis can be subtle but may include ipsilateral displacement of heart and mediastinum, absent hilar shadow, and volume loss of affected lung with hyperinflation of the contralateral lung [8]. Our patient's CXR demonstrated volume loss of the affected right lung but no hyperinflation of the contralateral lung nor other additional changes.…”

“…A substantial portion of congenital lung anomalies is detected early in childhood, frequently prenatally. Diagnosis is usually made in the setting of severe respiratory insufficiency or with the occurrence of acute respiratory infections later in childhood [8]. However, lung and pulmonary artery hypoplasia diagnosis is challenging in adults as they can easily be mistaken for more common diseases [4], and many patients survive into adulthood with minimal or no symptoms [9].…”