Unilateral congenital stenosis of the pulmonary veins

Binet, J P; Bouchard, Frédéric; Langlois, J; Chetochine, F; Conso, J F; Pottemain, M

doi:10.1016/s0022-5223(19)41898-9

Cited by 35 publications

(4 citation statements)

References 8 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…It may occur in the immediate postoperative period or as a late complication (Arciniegas el al., 198 1 ;Berman et af., 1977;Driscoll et al, 1977;Goodman er ul., 1976). Congenital obstruction of pulmonary venous return is rare, usually symptomatic, and frequently fatal, although unilateral obstruction may remain undiagnosed or manifest as chronic pulmonary disease for some time (Binet et al, 1972;Park et al, 1974;Sade et al, 1974). To our knowledge there is no report of the development of unilateral obstruction of pulmonary venous return following the Mustard procedure.…”

Section: Discussionmentioning

confidence: 99%

Hemoptysis following mustard repair: A late complication

Sapire

Casta

Hayden

et al. 1984

Clinical Cardiology

View full text Add to dashboard Cite

Summary:Hemoptysis was the presenting symptom in a 4-year, ll-month-old male who had had a Mustard operation for hemodynamic correction of transposition of the great vessels at the age of five months. Chest roentgenography demonstrated hyperlucency of the left lung and tomography showed compression and narrowing of left main stem bronchus. Angiography documented the absence of antegrade flow in the left pulmonary artery and no pulmonary venous drainage on the left. The left lung was supplied by bronchial collated arteries which drained by retrograde filling of the left pulmonary artery. It is surmised that pulmonary venous drainage on the left was compromised at surgery and that the dilated main pulmonary artery compressed the left main stem bronchus. This combination promoted bronchial collated ingrowth. Hemoptysis is a complication of enlargement of bronchial collateral vessels.

show abstract

Section: Discussionmentioning

confidence: 99%

Hemoptysis following mustard repair: A late complication

Sapire

Casta

Hayden

et al. 1984

Clinical Cardiology

View full text Add to dashboard Cite

show abstract

“…1) The first surgical repair of a CPVS was reported by Kawashima and colleagues in 1971. 18) Localized stenosis at the atrial junction has been treated in a few instances by patch grafting; 19) however, diffuse restenosis has been documented as a significant cause of late mortality after repair. 3) Due to the poor results of surgery for stenosis of the individual pulmonary veins, attempts to perform balloon angioplasty 17) or cutting balloon angioplasty 2) and utilization of balloon-dilatable stents have been reported.…”

Section: DI Is Sc Cu Us Ss Si Io On Nmentioning

confidence: 99%

Bilateral Congenital Pulmonary Vein Stenosis with a Normal Connection

Cho

Kim

Choi

et al. 2008

J Cardiovasc Ultrasound

View full text Add to dashboard Cite

緒言先天性肺静脈狭窄症（congenital pulmonary vein stenosis： CPVS）は，肺静脈が左房開口部で狭窄する疾患で，総肺静脈還流異常症，部分肺静脈還流異常症，三心房心などに合併することがある．その有病率は先天性心疾患の 0.03％ 1）と低く，特に，ほかに心内奇形のない孤立性肺静脈狭窄症（isolated pulmonary vein stenosis：IPVS）は，さらに稀である．病因は不明であり，進行性に肺高血圧（pulmonary hypertension：PH）が増悪するため，死亡率が高い 2）．今回，われわれは IPVS と診断され，二度にわたる手術後に PVS となり，経皮的肺静脈ステント留置術により救命した 1 乳児例を経験した．CPVS の臨床的特徴，治療法，予後因子について文献的考察を加え報告する． 1 Keywords： pulmonary vein stenosis, stent implantation, cardiac transcatheter intervention Congenital pulmonary vein stenosis is rare condition, and an isolated form of this condition characterized by no intra-cardiac anomalies is extremely rare. We report here a four-month-old male infant with bilateral pulmonary vein stenosis, who finally received a percutaneous stent implantation due to recurrent pulmonary vein stenosis after repeated surgical repair. Congenital isolated pulmonary vein stenosis is frequently lethal because of worsening pulmonary hypertension and cardiac failure. Surgical or transcatheter intervention is not a definite therapy due to recurrent stenosis. Although lung or cardiopulmonary transplantation might be recommended, there are limited cases in Japan. At present, percutaneous pulmonary vein stent implantation may be considered an important therapy as a bridge to cardiac transplantation. 要旨先天性肺静脈狭窄症（congenital pulmonary vein stenosis：CPVS）の頻度は低く，ほかの心奇形を合併しない孤立性肺静脈狭窄症（isolated pulmonary vein stenosis：IPVS）は極めて稀である．われわれは二度にわたる狭窄解除術を行ったが，肺静脈狭窄が再燃し，経皮的肺静脈ステント留置術により救命し得た IPVS の 1 例を経験した．乳児期発症の CPVS の予後は非常に悪く，外科手術，カテーテル治療の効果が乏しく，PVS が再燃し，高度肺高血圧（PH），心不全を来して死亡する．肺移植や心肺同時移植が推奨されるが，体格の成長を待つ必要があり，移植への bridging therapy として，経皮的肺静脈ステント留置術は選択肢の一つとなりうる． 2013 年 12 月 2 日受付 2014 年 3 月 18 日受理別刷請求先：〒 339-8551 埼玉県さいたま市岩槻区馬込 2100 埼玉県立小児医療センター循環器科藤本義隆日本小児循環器学会雑誌第30巻第３号 122 PEDIATRIC CARDIOLOGY and CARDIAC SURGERY VOL.30 NO.3 (343-349) 症例報告

show abstract

“…Abnormalities at later stages of development may result in cor triatriatum sinister, where either of the atria is divided by a thin membrane resulting in three atrial chambers. Disruptions to the cardiovascular development at very late stages might result in atresia of individual or the common PV [3][4][5][6].…”

Section: Introductionmentioning

confidence: 99%

Acquired unilateral pulmonary vein atresia in a 3-year-old boy

et al. 2014

View full text Add to dashboard Cite

While unilateral pulmonary venous atresia (UPVA) most commonly presents as an extremely rare late embryological defect resulting in complete occlusion or absence of the PV pathway, it may also be an acquired pathology. We present a 3-year-old boy who presented with mild respiratory distress. Neonatal echocardiographic investigations revealed normal mediastinal anatomy and pulmonary vasculature with a bicuspid aortic valve. However, follow-up Doppler investigation revealed a pulmonary artery size difference with minimal forward flow and reverse flow during diastole. Absence of the left pulmonary veins and the presence of collaterals draining to the innominate vein confirmed the diagnosis of acquired UPVA. Our case represents the first case of acquired UPVA in conjunction with a normally functioning bicuspid aortic valve. The Doppler flow patterns discussed might be of significant interest to pediatricians, cardiologists and imaging specialists. These findings suggest that acquired UPVA should be considered in the differential diagnosis of such patients when radiographic and echocardiographic findings may rule out other more common diagnoses. While the management of such a condition remains unclear and conservative management was agreed upon for our patient, the vulnerability of such cases warrants timely diagnosis and routine monitoring.

show abstract

Unilateral congenital stenosis of the pulmonary veins

Cited by 35 publications

References 8 publications

Hemoptysis following mustard repair: A late complication

Hemoptysis following mustard repair: A late complication

Bilateral Congenital Pulmonary Vein Stenosis with a Normal Connection

Acquired unilateral pulmonary vein atresia in a 3-year-old boy

Contact Info

Product

Resources

About