Unicuspid Aortic Valve

Thota, Venkata R.; Mookadam, Farouk

doi:10.5772/24280

Cited by 7 publications

(10 citation statements)

References 4 publications

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“…Adult patients with a UAV share many clinical features with patients with a BAV, including valvular dysfunction, aortic dilation, aortic dissection, and dysmorphic calcification. 1) 9) However, UAV patients generally show symptoms more earlier in their lives, usually in 30–50 years, and valvular dysfunction develops earlier and progresses at a faster pace in UAV patients than in aortic stenosis patients associated with a normal tricuspid AV. 1) 9) 10) One reported study showed that a smaller number of aortic cusps was associated with a greater incidence of valvular dysfunction or degeneration of the ascending aorta.…”

Section: Discussionmentioning

confidence: 99%

Severe Aortic Stenosis Associated with Unicommissural Unicuspid Aortic Valve in a Middle Aged Male

Kwon

Park

Kim

et al. 2016

J Cardiovasc Ultrasound

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Unicuspid aortic valve (UAV) is an extremely rare form of congenital aortic valvular abnormality. Although UAV shows similar clinical characteristics to bicuspid aortic valve, the clinical symptoms develop at earlier age and progress at a faster pace in UAV. In this report, we are presenting a 42-year-old male with severe aortic stenosis associated with unicommissural UAV. The patients underwent a successful Bentall operation.

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Section: Discussionmentioning

confidence: 99%

Severe Aortic Stenosis Associated with Unicommissural Unicuspid Aortic Valve in a Middle Aged Male

Kwon

Park

Kim

et al. 2016

J Cardiovasc Ultrasound

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“…On the other hand, unicommissural UAV which has one commissure with two rudimentary commissures with a broader valvular area, as in our patient, than that in acommissural UAV, is often asymptomatic until 30-50 years of age (17, 18). It is generally recognized that AS is common in UAV and primarily occurs earlier than AR (2,5). We considered that our patient initially had severe AS, which progressed to severe LF/LGAS with a gradually worsened LV function and valve cusp degeneration, which then led to the appearance of AR.…”

Section: Discussionmentioning

confidence: 99%

“…On the other hand, the unicommissural type often remains asymptomatic until adulthood. UAV is difficult to diagnose preoperatively (5) and is often associated with abnormalities of the aorta and/or cardiac malformations (2,(6)(7)(8)(9)(10)(11)(12). Compared with the bicuspid aortic valve (BAV), UAV is considered to progress more rapidly; therefore, a careful follow-up is necessary (5,10,13).…”

Section: Introductionmentioning

confidence: 99%

An Adult Case of Unicommissural Unicuspid Aortic Valve Diagnosed Based on the Intraoperative Findings

et al. 2016

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We herein report an adult case of unicommissural unicuspid aortic valve (UAV). A 59-year-old man, who was noted to have a cardiac murmur at 31 years of age, was admitted to our hospital due to acute heart failure. Severe calcification in the aortic valve with severe low-flow/low-gradient aortic stenosis and moderate aortic regurgitation was observed and thought to be the cause of heart failure, however, the etiology of aortic valve dysfunction was not clear. Aortic valve replacement was subsequently performed, and unicommissural UAV was diagnosed according to the intraoperative findings. UAV is very rare congenital aortic valve disease which is rarely diagnosed preoperatively.

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“…Also, the irregularly deposited calcific spurs may prevent the cusp from closing the orifice, thus AR may occur [1]. Adult UAV patients often have both AS and AR, while pediatric patients commonly present with AS alone [15, 36].…”

Section: Valvular Function and Clinical Presentationmentioning

confidence: 99%

“…In adult, the most common symptoms of UAV include dyspnea, angina, dizziness, and syncope [36]. Pediatric patients always present with left heart failure and failure to thrive.…”

Section: Valvular Function and Clinical Presentationmentioning

confidence: 99%

Unicuspid Aortic Valve: A Rare Congenital Anomaly

Jian-Hong¹

2021

Cardiology

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Unicuspid aortic valve (UAV) is a rare congenital aortic valve anomaly. It has two subtypes and often is associated with aortic valve dysfunction and corresponding clinical presentations. Echocardiography is the first choice of diagnostic method for UAV. Three-dimensional echocardiography has played an increasingly important role in diagnosis, intraprocedural guidance, and post-procedural assessment in recent years. There remain challenges in distinguishing UAV from bicuspid aortic valve (BAV) or tricuspid aortic valve (TAV). Misdiagnosis is most resulted from raphes or leaflet calcifications. Multi-modality imaging has obvious advantages over single-modality imaging and is crucial for UAV diagnosis. Accurate identification of aortic valve morphology is important to choose the best treatment. Aortic balloon valvoplasty, surgical valvotomy, commissurotomy, Ross procedure, surgical valve repair and surgical replacement are most common treatment modalities of UAV. In this review, we aim to discuss UAV including epidemiology, definition, classification, diagnostic importance and necessity, valvular function, clinical presentation, associated disorders, non-invasive diagnostic modalities and therapeutic approaches.

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Unicuspid Aortic Valve

Cited by 7 publications

References 4 publications

Severe Aortic Stenosis Associated with Unicommissural Unicuspid Aortic Valve in a Middle Aged Male

Severe Aortic Stenosis Associated with Unicommissural Unicuspid Aortic Valve in a Middle Aged Male

An Adult Case of Unicommissural Unicuspid Aortic Valve Diagnosed Based on the Intraoperative Findings

Unicuspid Aortic Valve: A Rare Congenital Anomaly

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