Type V congenital pouch colon: An extremely rare variant of anorectal malformations

Rawat, Jiledar; Singh, Sudhir; Pant, Nitin; Chaubey, Digamber

doi:10.4103/jiaps.jiaps_233_16

Cited by 3 publications

(3 citation statements)

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“…In this classification 4 types can be described, type I: normal colon is not present and the terminal ileum opens into the abnormal colon pouch, type II: the terminal ileum opens to the cecum which in turn opens to the colonic pouch, type III: there is a significant normal colonic segment between the ileum and the colonic pouch, and type IV: the colon is almost normal and the pouch involves the sigmoid and the rectum. Some authors describe a 5th type which is extremely rare and only few cases had been reported which consists of 2 colonic pouches with an intervening normal colonic segment [14,15].…”

Section: Discussionmentioning

confidence: 99%

Congenital pouch colon in Duhok, outcome and complications: Case series

Qadir

Mohammed

2019

Annals of Medicine and Surgery

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Background Congenital pouch colon (CPC) is a rare congenital abnormality associated with anorectal malformations with high incidence of complications and mortality. The aim of this study is to describe the various types of congenital colon pouch, their management aspects, complications of surgery, and the best management options. Results The incidence of congenital pouch colon in the present study was 5.3% (18 patients) of all anorectal malformations. Sixteen cases (88.8%) were males and 2 cases (12.5%) were females, (M: F ratio was 8:1). The age of presentation was ranged from 1day to 1year; 17 cases were presented in first week of life. Preoperative diagnosis of congenital pouch colon was done in 7 patients. As an initial procedure tabularization of the pouch with end colostomy was done in 15 cases, window colostomy was done in 2 cases, and excision of the pouch and proximal ileostomy was done in one patient. As a definitive procedure, abdomino-perineal pull-through of the tabularized pouch was done in 15 cases, ileo-anal anastomosis after pouch excision was done in 3 cases. Conclusions Pouch tabularization and end colostomy had better outcome than other types of interventions. Abdomino-perineal pull through of the tabularized pouch was the definitive surgical procedure for treatment of complete pouch colon in our study.

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Section: Discussionmentioning

confidence: 99%

Congenital pouch colon in Duhok, outcome and complications: Case series

Qadir

Mohammed

2019

Annals of Medicine and Surgery

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“…[1] Type V also has been described in the literature. [23] Type I is the most severe form and Type IV is the least. In males, the pouch usually terminates in a colovesical fistula just proximal to the bladder neck.…”

Section: Introductionmentioning

confidence: 99%

Type IV congenital pouch colon in male children: Anatomical variations and a proposed new subclassification

Solanki

Menon

Nayak

et al. 2020

J Indian Assoc Pediatr Surg

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Background:Congenital pouch colon (CPC) is a rare variant of anorectal malformation. In male patients, CPC communicates distally with the urogenital tract by a large fistula. The CPC cases which do not fulfill the criteria as mentioned in the classical description are reported along with the pertinent literature review.Materials and Methods:This was a retrospective study from January 2004 to December 2017 of male children with Type IV CPC. We evaluated clinical presentation, primary management, anatomical relationship, previous surgical intervention, definitive management, result, and outcome in terms of continence status on Templeton score.Results:Fifty-one children were included in the study among whom 36 children (Group 1) had a colovesical fistula and 15 children (Group 2) had no communication of the pouch with the genitourinary tract. In Group 2 children, the clinical presentations and management were varied: 4 underwent primary pull-through procedure, whereas 11 underwent staged procedure. Group 2 included three children in whom a narrow and thin-walled anal canal or anal canal with lower rectum was present, which was incorporated during the pull-through procedure. On continence assessment, only one child in Group 1 had “good” continence score compared to four children (three having anal canal) in Group 2.Conclusion:CPC Type IV can present without genitourinary tract communication (fistula), contrary to its emblematic description. Awareness about anatomical variations and adaptation of surgical technique accordingly is vital. The identification of the anal canal with or without the lower part of the rectum (even though apparently narrow and thin walled) and incorporation of this in bowel continuity lead to better outcomes in terms of continence.

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“…Классификация Narasimharao «ректального мешка»: CPC (congenital pouch colon) -врожденный «ректальный мешок»; SMA (Superior mesenteric artery) -верхняя брыжеечная артерия; UB (Urinary bladder) -мочевой пузырь; CVF (Colovesical fistula) -мочеполовой свищ[23] В 2008 году в классификацию был добавлен пятый вариант. Аномалия развития представляет собой несколько кишечных «мешков», между которыми находится нормально сформированный участок ободочной кишки[24].…”

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