Two-dimensional echocardiography and magnetic resonance imaging in diagnosis of idiopathic dilation of the right atrium

Iwase, Masatsugu; Hurui, Hirohiko; Miyaguchi, Kazuhiko; Hayashi, Hiroshi; Yokota, Mituhiro; Takeuchi, Jun; Ishiguro, Tuneo; Sakuma, Shinya

doi:10.1016/0002-8703(90)90145-n

Cited by 5 publications

(2 citation statements)

References 6 publications

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“…Later, in 1961, Pastor and Forte (1) described idiopathic enlargement of the right atrium. Several cases of IDRA (1,(3)(4)(5)(6)(7)(8) and familial IDRA (4) were reported in the ensuing years, but only one of these cases was reported as idiopathic dilatation of bilateral atria (2), and no cases were reported as idiopathic familial bilateral atrial dilatation (IFBAD).…”

Section: Discussionmentioning

confidence: 99%

An Autopsy Case of Familial Idiopathic Dilatation of Bilateral Atria.

et al. 1999

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A 59-year-old male patient was followed up for congestive heart failure. Echo cardiogram showed no abnormal findings other than a remarkable dilatation of the bilateral atria. The coronary arteries and left ventricular contraction were normal. Left ventricular endomyocardial biopsy showed no significant abnormal findings. Further, we examined his siblings using dynamic magnetic resonance imaging (MRI) and found that they all also had dilated bilateral atria. After several hospitalizations, the proband died from cardiogenic shock. Pathological findings showed nonspecific change in bilateral atria and ventricles. This is a very rare case of familial idiopathic dilatation of bilateral atria.

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Section: Discussionmentioning

confidence: 99%

An Autopsy Case of Familial Idiopathic Dilatation of Bilateral Atria.

et al. 1999

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“…Os achados anatomopatológicos consistem de uma dilatação aneurismática restrita ao AD, que é formado de paredes extremamente finas, com estudos histológicos mostrando extensa fibrose atrial. O diagnóstico da dilatação idiopática do AD é baseado nos achados ecocardiográficos característicos,5,6 sendo o diagnóstico diferencial feito principalmente com doenças que acometam o lado direito do coração, entre elas a anomalia de Ebstein e suas variações, a doença de Uhl e a displasia arritmogênica do VD. A anomalia de Ebstein apresenta implantação mais apical da valva tricúspide, acarretando maior dimensão do AD, suplantando inclusive o tamanho do ventrículo direito.…”

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Idiopathic Dilation of the Right Atrium in Asymptomatic Adolescent – Case Report

Costa¹,

Oliveira²,

Rodrigues³

et al. 2016

Arquivos Brasileiros De Cardiologia - Imagem Cardiovascular

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Management of Infants with Idiopathic Dilatation of the Right Atrium and Atrial Tachycardia

et al. 2007

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Idiopathic dilatation of the right atrium (IDRA) is a rare anomaly defined as isolated enlargement of the right atrium in the absence of other cardiac lesions known to cause right atrial dilatation. IDRA is a congenital anomaly with unknown pathogenesis and highly variable clinical presentation. Optimal management of severe IDRA is controversial and individualized. Literature reports of long-term follow-up have been limited. We describe a child with IDRA with rapid atrial tachycardia (AT) refractory to both medical and surgical management, and we provide long-term follow-up on our two previously reported cases, both of whom had documented AT. For infants with AT, the clinical course is unpredictable, and medical therapy is the first line of treatment. The decision to proceed with surgical resection of a giant right atrium should be made on an individual basis. Atrial resection along with a modified right atrial MAZE procedure could be considered in infants with life-threatening atrial tachyarrhythmia refractory to medical treatment. Surgical scarring of the right atrium may produce substrate for atrial arrhythmia, which may also be refractory to medical therapy. Histological examination of excised atrial tissue remains inconsistent and not contributory to the determination of the etiology of IDRA. Our three infants with IDRA illustrate unique features of their variable clinical courses, as well as continued difficulties with establishing clear guidelines with regard to surgical management of this unusual disorder.

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Two-dimensional echocardiography and magnetic resonance imaging in diagnosis of idiopathic dilation of the right atrium

Cited by 5 publications

References 6 publications

An Autopsy Case of Familial Idiopathic Dilatation of Bilateral Atria.

An Autopsy Case of Familial Idiopathic Dilatation of Bilateral Atria.

Idiopathic Dilation of the Right Atrium in Asymptomatic Adolescent – Case Report

Management of Infants with Idiopathic Dilatation of the Right Atrium and Atrial Tachycardia

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