Truncus Arteriosus Associated with Interrupted Aortic Arch in 50 Neonates: A Congenital Heart Surgeons Society Study

Long-term results after correction of persistent truncus arteriosus in 83 patients

“…In patients with IAA, the early mortality decreased from 66% to 13%. Sano and Jahangiri reported larger series of patients with PTA and IAA in which the repair was done without mortality but, in most studies, the mortality rate in this subset of patients with PTA is still high [10,17,18]. Late deaths in our series occurred in eight patients and all but one died in course of the first year after repair.…”

Survival and reintervention after neonatal repair of truncus arteriosus with valved conduit

“…However concern persists for newborns with truncus arteriosus and IAA. The poor prognosis for this group of patients has been confirmed by a multi-institutional Congenital Heart Surgeons Society study with a 10-year survival of 31% and high risk of reinterventions in survivors [8]. We recently analyzed our unsatisfactory results for truncus A4 according to Aristotle scoring and we concluded that patients with a score under 20 are likely to survive surgical repair [4].…”

Right Ventricular Outflow Tract Reconstruction in Patients With Persistent Truncus Arteriosus A 15-Year Experience in a Single Japanese Center

“…Since McGoon et al reported the first successful surgical repair of PTA using an aortic homograft in 1967, 2 incremental advances in surgical and perioperative management have resulted in a dramatic improvement in the outcome of this entity. [3][4][5][6][7][8] However, the overall outcome in patients with PTA is till compromised by associated anomalies, such as truncal valve insufficiency 9 or interrupted aortic arch, 10 and progressive obstruction of the conduit placed in the right ventricular outflow tract (RVOT) and associated peripheral pulmonary artery (PA) stenosis. [5][6][7]11 RVOT reconstruction in patients with PTA was initially achieved using a xenograft valved synthetic conduit in the 1980s, 11 and small homografts have become the first choice with the recognition of the advantages of elective neonatal repair of this lesion, especially in North American institutes.…”