Triatrial Heart with Persistent Ostium Primum and Cleft Mitral Valve

Horseshoe Lung With Cor Triatriatum and Partial Atrioventricular Canal Defect

“…Cor triatriatum in association with AVCD was first described in an autopsy specimen by Gahagan and Ziegler 1 in 1967. Since then, little more than ten cases of cor triatriatum have been reported with partial AVCD and fewer than five cases have been reported with complete AVCD.…”

“…This PAH is generally reversible after appropriate surgical management with good long-term outcome. 1,5 Presentation of patients with cor triatriatum and AVCD is usually delayed, and age of presentation depends upon the size of communication between the common chamber and the left atrium. 5 Size of communication >7 mm leads to delayed development of PAH while size of communication <3 mm causes early development of pulmonary venous and arterial hypertension.…”

The role of color-flow mapping in confirming the association of divided left atrium with an atrioventricular septal defect

“…As far as we know eight patients have been previously reported in association with an atrioventricular septal defect with separate atrioventricular orifices, mostly in anatomical'or surgical reviews. 3 " 8 It has also been shown that a dividing shelf is readily recognized using cross-sectional echocardiogram, and the pitfalls in echocardiographic evaluation have been v »ulJ *K emphasized. 2 ' 69 Pulsed Doppler studies can document turbulence when the communication in the abnormal atrial partition is obstructed.…”

Unique Combination of Atrioventricular Septal Defect With Cor Triatriatum and Complete Vascular Ring

“…Failure to address subdivided left atrium at the time of repair of an AVSD has been described, in association with postoperative mortality and a subsequent complete anatomic diagnosis at autopsy. 3 Thus, this defect should always be kept in mind during the diagnostic phase.…”