Transsphenoidal encephalocele, colpocephaly and corpus callosum agenesis in a midline cleft lip and palate patient: A very rare case

Dutta, Indranil; Sharma, Guruaribam Nilamani; Singh, Khungdombam Palin

doi:10.4103/ijps.ijps_118_18

Cited by 4 publications

(1 citation statement)

References 4 publications

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“…A basal encephalocele is defined as a neural element herniation, including the pituitary gland or optic chiasm, through an anatomical defect in the base of the skull [1][2][3][4]. They represent 1.5-5% of all cephaloceles, and the transsphenoidal encephalocele is the rarest form [2,5,6], with an incidence estimate of 1 in 700,000 live births [5][6][7]. Because of its rarity, the approaches to repair this congenital anomaly remain a challenge.…”

Section: Introductionmentioning

confidence: 99%

A hybrid simulation model for pre-operative planning of transsphenoidal encephalocele

et al. 2020

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Congenital transsphenoidal encephalocele (CTE) surgical correction is a challenging procedure. Although rare, this anomaly, characterized with neural herniation elements, including the pituitary gland or optic pathway through the sphenoid bone with anatomical alteration, can be presented in many different ways and should be individually analyzed. Significant advances in medical technology and the 3D models may simulate the complex anatomical relations of the human body. Nowadays, medical education relies on the availability of standardized materials that can reliably emulate human anatomy. Therefore, realistic anatomical models have become an alternative for cadavers or animal specimens. In this technical note, the authors present a new technique to create personalized models that combine 3D printing, molding, and casting to create an anatomically and tactilely realistic model based on magnetic resonance and computerized tomography images. Produced from different silicon types, the model recreated the anatomic alterations precisely, allowing a multidisciplinary team to determine the adequate surgical approach for this patient. We describe a case of congenital transsphenoidal encephalocele of a 3-year-old boy, whose surgical correction was planned using a hybrid model. The technical description of the model is given in detail. This new hybrid model allowed a detailed discussion of the surgical approach aspects by having tissues of different consistencies and resistances and a very high prediction rate. This approach may allow a reduction in surgery time and possible complications after operative procedures.

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Section: Introductionmentioning

confidence: 99%

A hybrid simulation model for pre-operative planning of transsphenoidal encephalocele

et al. 2020

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Persisting embryonal infundibular recess (PEIR) and transsphenoidal-transsellar encephaloceles: distinct entities or constituents of one continuum?

et al. 2022

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Trans-sellar–trans-sphenoidal encephalocele presenting as nasal obstruction in an infant: a case report and systematic review of existing reports

Basheer¹,

Raj²,

Mathew³

et al. 2023

Childs Nerv Syst

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Trans sellar trans sphenoidal encephalocele is a rare congenital anomaly, with only around 10 cases having been documented in literature around the world. Surgical repair of these defects in the pediatric population commonly uses either the trans cranial or the trans palatal approach, with the choice of approach being individualized based on the clinical features, age, and associated defects present in the patient. Here we document a case of a 4-month-old child who presented to us with nasal obstruction, who was diagnosed with this rare entity and successfully underwent a transcranial repair for the same.,

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Transsphenoidal encephalocele, colpocephaly and corpus callosum agenesis in a midline cleft lip and palate patient: A very rare case

Cited by 4 publications

References 4 publications

A hybrid simulation model for pre-operative planning of transsphenoidal encephalocele

A hybrid simulation model for pre-operative planning of transsphenoidal encephalocele

Persisting embryonal infundibular recess (PEIR) and transsphenoidal-transsellar encephaloceles: distinct entities or constituents of one continuum?

Trans-sellar–trans-sphenoidal encephalocele presenting as nasal obstruction in an infant: a case report and systematic review of existing reports

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