Transposition of the Great Arteries With Total Anomalous Pulmonary Venous Connection

Abstract

Transposition of the great arteries (TGA) with total anomalous pulmonary venous connection (TAPVC) is a rare association. Very few such cases have been reported. Among them 1 patient underwent anatomic repair. The rest received repair at the atrial level with either a modified Senning technique or a Mustard technique. We report a rare combination of TGA, TAPVC draining to the coronary sinus, and left juxtaposition of the atrial appendages with a diminutive right atrium. The anomalies were successfully repaired by anatomic correction.

Transposition of great arteries with total anomalous pulmonary venous connection: A modified Senning procedure for late presentation

“…Arterial switch operation (ASO) with repair of TAPVC is the ideal operation in this subset. 1 The balance between the pulmonary and systemic blood flow is a critical factor in the overall pathophysiology of CHD. An isolated shunt lesion can cause severe symptoms in any patient when associated with unbalanced systemic/pulmonary circulation, whereas complex lesions may be asymptomatic if associated with balanced systemic and pulmonary circulation, as seen in this subset of d-TGA.…”

A situs solitus transposition of great arteries with obstructed sub-diaphragmatic totally anomalous pulmonary venous connection: a rare case treated with anatomical repair

“…Transposition of the great arteries combined with totally anomalous pulmonary venous connection is extremely rare outside of heterotaxy syndrome. Since the first description in 1964, 1 few cases have been reported, [2][3][4][5][6][7][8][9][10][11] most have been treated by an atrial switch operation. We report the successful treatment of a neonate with transposition of the great arteries, intact ventricular septum and obstructed sub-diaphragmatic totally anomalous pulmonary venous connection, repaired by arterial switch operation and connection of the pulmonary venous return to the left atrium.…”

Complete transposition of great arteries associated with total anomalous pulmonary venous connection: An unusual cause for early left ventricular myocardial mass regression

“…[5] Recently, 2 more case reports of successful anatomic repair were reported in neonates. [67] In our case, we preferred to do atrial switch due to significantly small mitral valve annulus though some centers may still do ASO with extracorporeal membrane oxygenation support. In conclusion, complete TGA and TAPVC is a rare combination and should be suspected in cases with early LV regression along with dilated RA and RV and also in neonates presenting with high saturations with small inadequate mixing communications.…”