Tracheomegaly in association with rheumatoid arthritis

Çelenk, Çetin; Çelenk, Peruze; Selçuk, Mustafa Bekir; Özyazici, B.; Kuru, Ömer

doi:10.1007/s003300000451

Cited by 10 publications

(4 citation statements)

References 7 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Several case reports mention congenital defects, including accessory tracheal bronchi [S19,S27,S29,S51], but as for one report [S51] the airway size is not given, the criteria for the syndrome can't be verified. TBM has been described in 3 [13,14]. In a child with Ehlers-Danlos syndrome [S59] the airway size didn't quite reach the criteria for MKS but it can't be excluded that the trachea might have enlarged further reaching the necessary criteria of TBM.…”

Section: Associations With Other Diseasesmentioning

confidence: 99%

Mounier-Kuhn syndrome or congenital tracheobronchomegaly: A literature review

Krustiņš

Kravale

Buls

2013

Respiratory Medicine

124

View full text Add to dashboard Cite

Mounier-Kuhn syndrome or congenital tracheobronchomegaly is a chronic airway condition which for currently unknown reasons mostly affects males. It is commonly overlooked on conventional chest X-rays, and is considered to be rare, but the prevalence might be higher as commonly assumed. The hallmark of it is a dilatation of the main airways which frequently, but not always, causes marked, mainly respiratory, symptoms, and patients usually present with varying degrees of recurrent infections, breathlessness, haemoptysis, dyspnoea. Although at least 200 case reports have been published, there have been only a few attempts to review them, and none in the last 20 years. Due to the lack of clinical trials and wide variability of case-report format, a systematic review was deemed not feasible, therefore PubMed and Medline databases were searched using terms "Mounier-Kuhn syndrome", "tracheobronchomegaly", "tracheomegaly", and "bronchomegaly", without any time restrictions, to summarize currently known facts about the syndrome. To the authors' best knowledge, the result is currently the most comprehensive review of previously published literature about the congenital tracheobronchomegaly, and summarizes what's known about symptoms, prevalence, disease associations, and treatment options for this syndrome.

show abstract

Section: Associations With Other Diseasesmentioning

confidence: 99%

Mounier-Kuhn syndrome or congenital tracheobronchomegaly: A literature review

Krustiņš

Kravale

Buls

2013

Respiratory Medicine

124

View full text Add to dashboard Cite

show abstract

“…Reconstructive methods including multiplanar imaging and virtual bronchoscopy have made a significant impact on diagnosis and management of patients. 15 MKS has been associated with other connective tissue diseases like Marfan syndrome, Ehlers-Danlos syndrome, ankylosing spondylitis and rheumatoid arthritis, [16][17][18] the patient presented in this case had no features to suggest any of the above connective tissue disorders. Unfortunately, we were unable to perform genetic tests that would have helped us to exclude these differentials due to the limited access of these tests in our setting.…”

Section: Echocardiogrammentioning

confidence: 71%

Tracheobronchomegaly (Mounier-Kuhn Syndrome) in a 43-Year-Old Male: A Case Report

Babirye¹,

Walubembe²,

Babirye³

et al. 2022

IMCRJ

View full text Add to dashboard Cite

Mounier-Kuhn syndrome (MKS) or congenital tracheobronchomegaly is a rare disorder characterized by marked dilatation of the trachea and main bronchi, bronchiectasis, and recurrent respiratory tract infections. The etiology of this disorder is uncertain and the clinical presentation is variable. The diagnosis is usually made based on the characteristic computed tomography (CT) scan findings. This report describes a case of a 43-year-old man presenting with persistent cough and recurrent lower respiratory tract infections since childhood associated with copious amounts of purulent sputum, difficulty in breathing, and weight loss. In addition, he reported palpitations, dyspnea, orthopnea, abdominal and lower limb swelling. The chest X-ray showed a dilated trachea (35mm) and bronchi (26mm (right) and 27mm (left)) with cystic bronchiectasis and reticulolinear opacities predominantly involving the middle and lower lung zones. Chest CT scan confirmed the diagnosis of MKS as evidenced by dilated trachea and bronchi complicated by diverticula formation. Electrocardiogram, echocardiography and abdominal ultrasound scan showed features of right-sided heart failure secondary to pulmonary hypertension. MKS, although rare, should be considered as a possible diagnosis in patients presenting with productive chronic cough, recurrent pneumonia, or incomplete response to appropriate antibiotic therapy for pneumonia.

show abstract

“…Tracheomegaly is diagnosed when the transverse diameter of the trachea exceeds 25 mm and 21 mm in men and women, respectively. 2 , 3 In this report, the maximum transverse diameter was measured to be 43 mm on CT scan.…”

Section: Discussionmentioning

confidence: 91%

Tracheomegaly Secondary to Tracheotomy Tube Cuff in Amyotrophic Lateral Sclerosis

et al. 2015

View full text Add to dashboard Cite

Tracheomegaly has not been reported in amyotrophic lateral sclerosis (ALS). Herein, the authors report a case of tracheomegaly secondary to tracheotomy tube cuff in a patient with ALS. To our knowledge, this is the first report of an ALS patient with tracheomegaly and of tracheomegaly being associated with tracheotomy tube cuff and home tracheotomy mechanical ventilator.The clinician should consider the possibility of tracheomegaly in the differential diagnosis, if a patient with ALS develops repeat air leakage around the tracheotomy tube or rupture of tracheotomy tube cuff.

show abstract

Tracheomegaly in association with rheumatoid arthritis

Abstract: Herein we present a case of tracheomegaly seen in a patient with rheumatoid arthritis. To the authors' knowledge, and from a review of the literature, this combination has not been previously described.

Cited by 10 publications

References 7 publications

Mounier-Kuhn syndrome or congenital tracheobronchomegaly: A literature review

Mounier-Kuhn syndrome or congenital tracheobronchomegaly: A literature review

Tracheobronchomegaly (Mounier-Kuhn Syndrome) in a 43-Year-Old Male: A Case Report

Tracheomegaly Secondary to Tracheotomy Tube Cuff in Amyotrophic Lateral Sclerosis

Contact Info

Product

Resources

About