Thromboembolic complications in patients with arrhythmogenic right ventricular dysplasia/cardiomyopathy

Abstract

(i) ARVD/C may be complicated by thrombosis. Annual incidence of such complications is significantly lower than reported for left ventricle failure. (ii) Anticoagulation should be used in ARVD/C patients with large, hypokinetic RV and slow blood flow. (iii) Patients with severe forms of ARVD/C, thrombus formation in the RV and/or spontaneous echocardiographic contrast are at higher risk of a poor outcome.

Isolated ventricular noncompaction mimicking arrhythmogenic right ventricular cardiomyopathy — A study of nine patients

“…Palpitations are usually reported to be the first symptom of either IVNC or ARVC. However, atrial fibrillation (AF) is observed in more than 25% of all patients with IVNC, whereas in ARVC this arrhythmia is associated with advanced stages of the disease [15]. In our study group AF was the first symptom of the disease in 2 cases with mildly damaged RV.…”

Massive Right Atrial Thrombus Formation Followed by an Atrial Flutter with 1:1 Atrioventricular Conduction in a Patient with Arrhythmogenic Right Ventricular Cardiomyopathy

“…It has recently been reported that the prevalence of atrial tachyarrhythmias such as atrial fibrillation (AF) and atrial flutter (AFL), which are well-known as important causes of atrial thrombus formation, are common and occur in 14% of patients with ARVC (2). However, the incidence of thromboembolic complications in patients with ARVC is very low (3). We herein report a case of a massive right atrial thrombus associated with tachycardiac AFL in a patient with ARVC.…”

Arrhythmogenic Right Ventricular Cardiomyopathy

“…Treatment consists of diuretics, angiotensin-converting enzyme inhibitors and digitalis, as well as anticoagulants. 2,3 In the retrospective study by Wlodarska et al 99 of 126 ARVC patients followed-up for a mean period of 99±64 months, the annual incidence of thromboembolism was 0.5%. It is still debated whether prophylactic anticoagulation is needed in patients with RV aneurysms and with the left-dominant and biventricular subtypes of ARVC.…”