The vascular "ring" sign in mesoblastic nephroma: report of two cases

Abstract

Mesoblastic nephroma (Bolande's tumour) is a rare renal tumour, but, overall, is the most frequent benign renal tumour in childhood and the most frequent renal tumour during the first year of life. It is increasingly diagnosed with US during the fetal period. We report the findings of two patients who showed the "ring" sign, an anechoic ring surrounding the tumour and typical of mesoblastic nephroma. We identified a Doppler signal in the ring in both cases, and pathology confirmed the vascular origin of this sign.

An Approach to Renal Masses in Pediatrics

“…21,104,105 A concentric hyperechoic and hypoechoic ring pattern known as the vascular "ring" sign may also be seen surrounding the tumor. 106 Postnatal CT typically reveals a large, heterogeneous, solid intrarenal mass with smooth margins that enhances to a lesser degree than the adjacent normal renal parenchyma after intravenous contrast administration (Fig 8). 7,104 Based on histopathologic appearances, congenital mesoblastic nephroma is subtyped into classic (24%), cellular (66%), and mixed (10%) types.…”

Congenital Mesoblastic Nephroma Presenting with Neonatal Hypertension

“…The hypoechoic ring surrounding the tumor with a Doppler signal indicating blood flow can be confirmed by pathology to be vascular. 6,8 Wilms' tumor manifests as a solid intrarenal mass with a pseudocapsule and distortion of the renal parenchyma and collecting system. It does not typically encase or elevate the aorta as does a neuroblastoma.…”

“…To date, only nine patients with CMN and hypertension have been reported, out of which six were neonates. 5,6 We describe the clinical presentation and discuss the findings on abdominal imaging in a 30-week gestation infant with hypertension and CMN.…”

Bildgebende Differenzierung des Rhabdoidtumors vom Nephroblastom und mesoblastischen Nephrom

“…Das MN ist der typische Nierentumor im . Lebensjahr, jedoch wurde auch von 22 Fällen bei Erwachsenen berichtet [8]. In der Regel werden Patienten mit MN alleine durch Operation geheilt.…”