The sensitivity of this parameter was 97%, specificity was 81%, and negative predictive value was 99%. T wave inversion in lead V1 with an amplitude of ≥2 mm The same author presented this marker as a typical finding in patients with arrhythmogenic cardiomyopathy also in cases with T wave inversion only in lead V1 [8]. Children below the age of 14 years were excluded, the mean age of this cohort was 46.8±11.8 years. In bipolar precordial leads, a T wave inversion of ≥3 mm in lead V1 has been described as a typical finding [9]. Controlled by the same number of normal probands, the sensitivity was 93%, specificity was 97%, and negative predictive value was 99%. Combination of the above-mentioned features If typical ECG abnormalities in lead aVR and T wave inversion in lead V1 were combined, the sensitivity was 94%, specificity was 99%, and negative predictive value was 99.9% [10,11]. QRS fragmentation in all leads Fontaine described QRS fragmentation as "pre"-, "top"-, and "post"-silon in patients with typical arrhythmogenic cardiomyopathy in high values [12]. QRS fragmentation is an unspecific finding and can be described in a large number of other diseases like hypertrophic or dilated cardiomyopathy, long QT syndrome, and Brugada syndrome [13]. Conclusions There are indeed ECG parameters of concealed arrhythmogenic cardiomyopathy which enable the diagnosis at a very early phase. Ajmaline challenge in an early stage is positive in some cases. These are patients with a very high risk of ventricular fibrillation described by Corrado [14] and Peters [15]. Perhaps these are those patients with sudden cardiac death as the first manifestation of the disease.