The role of echocardiography in diagnosing double chambered right ventricle in adults

Abstract

Patients: 32 patients, mean age 32.5 years, 21 female, and 11 male. Intervention: Transthoracic (TTE) and transoesophageal (TOE) echocardiographic examination in patients with suspected DCRV. Main outcome measures: Direct inspection during surgical treatment of 28 patients diagnosed as having DCRV as an isolated lesion or associated with other pathologies. Results: Echocardiography allowed the final diagnosis of DCRV in 26 patients (81%) out of 32 studied. TTE was diagnostic in 5 (15.6%) whereas TOE was diagnostic in 21 of 21 studied by this technique. Of 6 patients with negative TTE, DCRV was identified by cardiac catheterisation in 3 and directly during surgery in the remaining 3. Of 26 patients diagnosed by echocardiography, the anomalous muscle bundle was discrete in 20 (77%) and diffuse in 6 (23%). In 23 patients (88%) right ventricular outflow obstruction was localised low in the right ventricle, and in the remaining 3 (11.5%), the obstruction was localised high in the right ventricle. Abnormal bundles localised high were discrete, bundles localised in the lower part of right ventricle were discrete in 17 (74%) and diffuse in the remaining 6 (26%). DCRV was an isolated lesion in only 2 patients (6.2%). In all subjects surgical inspection confirmed echocardiographic data. Conclusions: Echocardiography was very useful to diagnose DCRV in adults as well as to identify its anatomic type. Comparing two different approaches, TOE better defines the entire scope of pathology, including estimation of the resultant systolic pressure gradient within the right ventricular cavity.

Erişkin bir hastada çift odacıklı sağ ventrikül ve ciddi koroner arter hastalığı: Olgu sunumu

“…Daha önceki çalışmalar transtorasik ekokardiyografi ile erişkinlerdeki çift odacıklı sağ ventrikül olgularının yalnızca %8-17 oranında doğru tanı koyulabileceğini göstermiştir [6,14,15]. Bu olgularda transezofageal ekokardiografi ve kalp kateterizasyonu yapılması tavsiye edilmektedir.…”

Renal coloboma syndrome associated with double- chambered right ventricle

“…During the 4 th to 7 th weeks, the heart undergoes into a typical four-chambered structure with endocardial cushions, which have critical role in many cardiac deformities (5). DCRV is relatively rare as an isolated anomaly (approximately 0.5-2% of CHD) with no inheritance pattern (6). Patients with DCRV frequently have other congenital cardiac anomalies.…”

Przypadek dwujamowej prawej komory rozpoznanej na podstawie badania metodą rezonansu magnetycznego i cewnikowania

“…Cardiac magnetic resonance imaging and invasive testing can provide further information to confirm the diagnosis and guide therapeutic decisions [5]. Many authors have reported a high incidence of concomitant congenital disease; up to 90% of cases are associated specifically with membranous-type ventricular septal defects [6].…”

“…The most effective form of diagnosis of DCRV is TEE [6]. Use of continuous Doppler also allows for the calculation of intraventricular pressure gradients and obviates the need for additional cardiac catheterization [6,7]. On echocardiography, fibrotic and hypertrophic tissue is more evident during systole, since the muscle bands are contracted and thickened [8].…”