P ulmonary hypertension (PH) is a progressive and ultimately fatal disease that presents as an elevated blood pressure in the pulmonary arteries. PH evolves as a comorbidity of other diseases or conditions, such as connective tissue diseases, lung diseases, liver disease, pregnancy, HIV infection, left heart failure, and the usage of the diet medication Fen-Phen, a combination of the 2 drugs fenfluramine (Pondimin) and phentermine (Lonamin). Although triggered by other diseases or conditions, the specific etiology of PH is not known. PH and comorbidity conditions affect a diverse segment of the population.The demographic profile of adult PH patients includes men and women of all ages, racial, and ethnic groups. Between 2000 and 2002, the Centers for Disease Control and Prevention reported 807,000 adults were hospitalized with PH. Of these adults, 61% were women and 66% were 65 or older. 1 During the time period of 1980-2002, the number of PH deaths increased from 10,922 to 15,668, respectively; however, the greatest increase was observed only among women. 1 Among all racial populations, the number of adult PH deaths has increased mostly among the African American population. 1 Death rates are higher among the elderly, especially men 85 or older, women 65 or older, whites 75 or older, and African Americans 65 or older. 1 Regardless of gender, age, or race, PH patients require continuous evaluation and management by an interdisciplinary team to alter disease progression and the resultant impact on multiple organ systems.PH affects both the pulmonary and cardiovascular systems, with a potential negative impact on quality of life. PH patients have many acute and chronic health care needs that require meticulous evaluation, management, and care coordination. The nurse practitioner (NP) collaborates within an interdisciplinary team to effectively
ABSTRACTThe prevalence of adult pulmonary hypertension (PH) in the United States has escalated in all races, gender, and ethnic populations. Nurse practitioners (NPs) are encountering adults with PH with increasing frequency. Through increased knowledge of the pathophysiological changes, diagnostic measures, and treatments for adults with PH, NPs collaborate with interdisciplinary teams to manage and improve client outcomes and quality of life.