The Prevalence of Marfan Syndrome in Korea

Jang, Shin Yi; Seo, Su Ra; Park, Seung Woo; Kim, Duk Kyung

doi:10.3346/jkms.2017.32.4.576

Cited by 11 publications

(7 citation statements)

References 14 publications

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“…The differences in characteristics were analyzed using the Student's t-test for continuous variables and the χ 2 test for categorical variables. The age-standardized prevalence and incidence of TAO were calculated with the direct method using the beneficiaries of health insurance from the Korean National Health Insurance Statistical Yearbook from 2006 through 2017 and the estimated Korean population in 2015 as a reference (4). The Kaplan-Meier method was also used with log-rank tests to compare survival among patients with TAO by age group and sex.…”

Section: Discussionmentioning

confidence: 99%

The incidence, prevalence, and survival rate of thromboangiitis obliterans in Korea: a retrospective population-based study

Choi¹,

Jang²,

Kim³

et al. 2020

Cardiovasc Diagn Ther

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Background: Few studies used nationwide data to assess the age-standardized prevalence rate, incidence rate, 10-year survival rate, and death risk of thromboangiitis obliterans (TAO; Buerger's disease).Methods: Data for 24,392 patients who had newly diagnoses related to TAO (I73.1) from 2006 through 2017 were extracted from the National Health Insurance Service in Korea. The age-standardized prevalence rate, incidence rate, 10-year survival rate, and death risk of TAO were analyzed. Results: The mean (standard deviation) age of TAO patients overall was 62.0 (15.7) years; 61.3 (15.4) in males and 63.2 (16.1) in females (P<0.001). The proportion of patients older than 50 years old was about 80% overall. The proportion patients who died of TAO was 28.1%. Overall, the age-standardized prevalence rate of TAO decreased from 11.1 persons per 100,000 persons in 2006 to 8.43 persons in 2017, and overall, the incidence rate of TAO decreased from 6.07 persons in 2006 to 3.38 persons in 2017. Theage-standardized prevalence rate and incidence rate in males were higher than that in females. The 10-year survival rate of TAO was about 65% (60.7% in males and 72.5% in females). The adjusted hazard ratio increased significantly with older age, male sex, hypertension, diabetes mellitus, myocardial infarction, heart failure, ischemic stroke, hemorrhagic stroke, chronic kidney disease, and malignant neoplasm. Conclusions:The 10-year survival rate of TAO was about 65%. Even though the age-standardized prevalence rate and incidence rate of TAO is decreased during the study period, the adjusted hazard ratio showed significantly increases with age and with male sex after adjustment for comorbidities.

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Section: Discussionmentioning

confidence: 99%

The incidence, prevalence, and survival rate of thromboangiitis obliterans in Korea: a retrospective population-based study

Choi¹,

Jang²,

Kim³

et al. 2020

Cardiovasc Diagn Ther

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“… 10 We calculated the age-standardized incidence rates (incidence rate) of ACHD, AF in ACHD, and AF in the Korean general population with the direct method 16 using the beneficiaries of health insurance from the Korean National Health Insurance Statistical Yearbook from 2006 through 2015 and the estimated Korean population in 2015 as the reference. 17 In addition, the incidence rate of AF in ACHD with the direct method was calculated using age groups according to the direct method using a decade of ACHD data as a reference. The Kaplan-Meier method was used to compare survival among patients with ACHD according to AF, AF by age group, and AF by sex using the log-rank or Wilcoxon tests.…”

Section: Methodsmentioning

confidence: 99%

Impact of Atrial Fibrillation on Survival in Adults with Congenital Heart Disease: a Retrospective Population-based Study

et al. 2021

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Background The number of adults with congenital heart disease (ACHD) with atrial fibrillation (AF) is expected to increase. We sought to assess the impact of AF on survival in Korean ACHD. Methods Records of AF in ACHD were extracted from the records of the Korea National Health Insurance Service from 2006 through 2015. Multiple Cox proportional hazards analyses were carried out after adjustment for age, sex, income level, AF, and comorbidities. Survival rates (SRs) with and without AF were compared. The death records from 2006 through 2016 were included. Results A total of 3,999 ACHD had AF (51.4% were male) and 62,691 ACHD did not have AF (43.5% were male); the proportion of ACHD who were 60 years and older was 53.0% and 27.0% in those with and without AF, respectively ( P < 0.001). The age-standardized incidence rate for AF was 1,842.0 persons per 100,000 people in the Korean general population from 2006 through 2015. For AF in ACHD, it was 5,996.4 persons per 100,000 ACHD during the same period, which was higher than that in the general population ( P < 0.001). Significantly higher proportion of death (20.9%) occurred in ACHD with AF than without AF (8.3%) ( P < 0.001). The adjusted hazard ratio for AF of death in ACHD was 1.39 (95% confidence interval, 1.29–1.50). The ten-year SR of ACHD with AF was 69.7% whereas it was 87.5% in non-AF ( P < 0.001). Conclusion In ACHD, AF occurs more frequently and has a worse prognosis than seen in the non-valvular general population in Korea. AF is associated with increased death in ACHD, especially with aging.

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“…The age-standardized prevalence of amyloidosis was calculated with the direct method [ 11 ] using the beneficiaries of health insurance from the Korean National Health Insurance Statistical Yearbook from 2006 through 2015 [ 12 – 21 ] and the estimated Korean population in 2015 [ 22 ] as a reference [ 23 , 24 ].…”

Section: Methodsmentioning

confidence: 99%

Prevalence of Amyloidosis in Korea

Seo

Jang

Lee

et al. 2017

Orphanet J Rare Dis

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BackgroundThe aim of this study was to assess in amyloidosis prevalence in Korea between 2006 and 2015.MethodsPrimary diagnoses related to amyloidosis, regardless of subtype, were collected from the Korean National Health Insurance Service from 2006 through 2015.ResultsOverall, the age-standardized prevalence of amyloidosis was 0.93 (95% confidence interval (CI) 0.81, 1.04) persons per 100,000 persons in 2006 and 1.91 (95% CI 1.78, 2.05) persons per 100,000 persons in 2015. This included an increase from 0.43 (95% CI 0.35, 0.51) to 1.04 (95% CI 0.94, 1.14) persons per 100,000 persons in men and from 0.49 (95% CI 0.40, 0.57) to 0.87 (95% CI 0.77, 0.96) persons per 100,000 persons in women. In particular, the age-standardized prevalence of amyloidosis showed a greater increase in patients aged 65 years or older and in patients aged 45–64 years than in patients aged 20–44 years, for both men and women.ConclusionsThe overall age-standardized prevalence of amyloidosis was approximately 2 persons per 100,000 persons in 2015. The overall age-standardized prevalence of amyloidosis increased between 2006 and 2015, especially in individuals aged 45–64 and older than 65 years.Electronic supplementary materialThe online version of this article (10.1186/s13023-017-0705-2) contains supplementary material, which is available to authorized users.

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The Prevalence of Marfan Syndrome in Korea

Cited by 11 publications

References 14 publications

The incidence, prevalence, and survival rate of thromboangiitis obliterans in Korea: a retrospective population-based study

The incidence, prevalence, and survival rate of thromboangiitis obliterans in Korea: a retrospective population-based study

Impact of Atrial Fibrillation on Survival in Adults with Congenital Heart Disease: a Retrospective Population-based Study

Prevalence of Amyloidosis in Korea

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