The Management of Chest Wall Resection in a Patient With Polyostotic Fibrous Dysplasia and Respiratory Failure

O'Connor, Brendan; Collins, Frank J.

doi:10.1053/j.jvca.2008.09.009

Cited by 10 publications

(6 citation statements)

References 9 publications

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“…Fibrous dysplasias are benign tumors that affect the ribs in 50% of cases, 70% are solitary and 25% can be polyostotic. 4 In 5% of cases, they may be associated with cafe ´-au-lait spots and precocious puberty, known as McCune-Albright syndrome. 4 Although the tumors are generally benign, malignant transformation has been reported from 0.4% to 4%.…”

Section: Discussionmentioning

confidence: 99%

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Polyostotic rib fibrous dysplasia resected by video-assisted thoracoscopic surgery with preservation of the overlying periosteum

Shim

Chon

Lee

et al. 2010

The Journal of Thoracic and Cardiovascular Surgery

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Video-assisted thoracoscopic rib resection has rarely been reported, but a relatively simple procedure that uses readily available instruments can prove to be feasible. [1][2][3] A conventional approach would involve an incision greater than the length of the mass itself. Such an approach would require significant resection of the chest wall musculature and could lead to significant postoperative morbidity and decrease in quality of life. Multiple rib tumors would require an even more extensive incision and may require multiple incisions to facilitate exposure and removal. We report the removal of 2 expansile bone tumors by video-assisted thoracoscopic surgery while preserving the periosteum to allow for bone formation. To the best of our knowledge, no such attempts at preserving the periosteum during a rib resection via video-assisted thoracoscopy have been done. CLINICAL SUMMARYAn 18-year-old male patient with Down syndrome was admitted to the urology department of Hanyang University Guri Hospital with a testicular artery rupture after a bicycle accident. The patient underwent an emergency operation for the bleeding. After a thorough inquiry, the patient reported having chest pain over his left chest wall for 3 months. The patient did not have precocious puberty or cafe ´-au-lait spots. A routine chest x-ray showed cortical thickening in the patient's ribs. Computed tomography scans of his chest showed multiple bone tumors of the fourth, sixth, seventh, and eighth ribs (Figure 1). The sixth and seventh ribs were expansile; thus, for diagnostic reasons and to rule out possible malignancy, he was referred to the general thoracic department and an operation by minimally invasive surgery was scheduled.General anesthesia was done with double-lumen ventilation, and the patient was placed in the right down 30-degree semilateral position with his right arm tucked beside the pillow. Three ports were used: a 3-mm port at the third intercostal space, a 15-mm port at the areola margin, and a 5-mm

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Section: Discussionmentioning

confidence: 99%

“…4 In 5% of cases, they may be associated with cafe ´-au-lait spots and precocious puberty, known as McCune-Albright syndrome. 4 Although the tumors are generally benign, malignant transformation has been reported from 0.4% to 4%. 5 Our particular case presented 4 bone lesions, 2 of which were expansile.…”

Section: Discussionmentioning

confidence: 99%

Polyostotic rib fibrous dysplasia resected by video-assisted thoracoscopic surgery with preservation of the overlying periosteum

Shim

Chon

Lee

et al. 2010

The Journal of Thoracic and Cardiovascular Surgery

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“…Fibrous dysplasias are benign tumors of which more than 50% are located on the ribs. Even though the majority of the tumors are benign, malignant transformation has been reported in 0.4% to 4% of tumors [3,4]. Like all the other benign neoplasms, the main principle for surgical approach consists of wide resection of the involved ribs with clear margins.…”

Section: Commentmentioning

confidence: 99%

Total Rib Resection Via Uniportal Thoracoscopic Approach

Ocakcıoğlu

Ermerak

Yüksel

2018

The Annals of Thoracic Surgery

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In this report, we present a case specifying the availability of uniportal thoracoscopic resection of a total rib safely without the need for conventional thoracotomy. The favorable outcome of this case suggests that the uniportal thoracoscopic technique described here is a safe and successful approach for resection of costal lesions with good cosmetic results. To our knowledge, this is the first case reporting the entire rib resection via uniportal thoracoscopic approach.

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“…Fibrous dysplasia (FD) of bone is a rare, non-inheritable congenital disease characterized by a focal proliferation of fibrous tissue in bone marrow [1]. FD can affect any bone but those most commonly involved are the femur, tibia, fibula, and the bones of the skull and pelvis [2]. Cases of sternal FD have rarely been reported.…”

mentioning

confidence: 99%