The longitudinal follow up of a universal neonatal hearing screen: The implications for confirming deafness in childhood

Watkin, Peter; Baldwin, Margaret

doi:10.3109/14992027.2012.673237

Cited by 83 publications

(48 citation statements)

References 32 publications

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“…7 On the basis of these programmes, the estimated prevalence of permanent bilateral hearing loss is 1.33 per 1,000 live births. 9 In children of primary school age, the prevalence increases to 2.83 per 1,000 children, 10, 11 with a further increase to 3.5 per 1,000 in adolescents. 9 This increase over time presumably reflects the cumulative addition of patients with hearing loss owing to progressive, acquired or late-onset genetic causes.…”

Section: Epidemiologymentioning

confidence: 99%

Congenital hearing loss

Korver

Smith

Camp

et al. 2017

Nat Rev Dis Primers

398

310

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Congenital hearing loss (hearing loss present at birth) is one of the most prevalent chronic conditions in children. In the majority of developed countries, neonatal hearing-screening programmes enable early detection; early intervention will prevent delays in speech and language development and have long-lasting beneficial effects on social and emotional development and quality of life. A hearing loss diagnosis is usually followed by a search for an underlying aetiology. Congenital hearing loss might be attributed to environmental and prenatal factors, which prevail in low-income settings; congenital infections, particularly cytomegalovirus, are also a common risk factor for hearing loss. Genetic causes probably account for the majority of cases in developed countries; mutations can affect any component of the hearing pathway, in particular inner ear homeostasis (endolymph production and maintenance) and mechano-electrical transduction (conversion of a mechanical stimulus into electrochemical activity). Once the underlying cause of hearing loss is established, it might direct therapeutic decision-making and guide prevention and (genetic) counseling. Management options include specific antimicrobial therapies, surgical treatment of cranio-facial abnormalities and hearing aids. An improved understanding of the pathophysiology and molecular mechanisms underlying hearing loss and increased awareness of recent advances in genetic testing will promote the development of new treatment and screening strategies.

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Section: Epidemiologymentioning

confidence: 99%

Congenital hearing loss

Korver

Smith

Camp

et al. 2017

Nat Rev Dis Primers

398

310

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“…About 1 in 500 babies are born with permanent hearing loss, making it one of the one of the most common birth defects in developed countries (Ross et al, 2008; Watkin and Baldwin, 2012). About 8,000 children are born in the United States each year with congenital hearing loss (White, 2008).…”

Section: Introductionmentioning

confidence: 99%

“…About 8,000 children are born in the United States each year with congenital hearing loss (White, 2008). In the past decade, universal newborn hearing screening (NHS) has reduced the mean age of diagnosis of all hearing loss from about 30 months prior to universal newborn screening to about 3-4 months in 2009 (Harrison and Roush, 1996; CDC, 2011; Watkin and Baldwin, 2012). In order to achieve the best outcomes for NHS programs, early and accurate diagnosis of congenital hearing loss is essential to allow appropriate and early intervention in order to lessen developmental sequelae (JCIH, 2007).…”

Section: Introductionmentioning

confidence: 99%

Air and Bone Conduction Click and Tone-Burst Auditory Brainstem Thresholds Using Kalman Adaptive Processing in Nonsedated Normal-Hearing Infants

et al. 2015

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Objective To study normative thresholds and latencies for click and tone-burst auditory brainstem response (TB-ABR) for air and bone conduction in normal infants and those discharged from neonatal intensive care units (NICU), who passed newborn hearing screening and follow-up DPOAE. An evoked potential system (Vivosonic Integrity™) that incorporates Bluetooth electrical isolation and Kalman-weighted adaptive processing to improve signal to noise ratios was employed for this study. Results were compared with other published data. Research Design One hundred forty-five infants who passed two-stage hearing screening with transient-evoked otoacoustic emission (OAE) or automated ABR were assessed with clicks at 70 dB nHL and threshold TB-ABR. Tone-bursts at frequencies between 500 to 4000 Hz were employed for air and bone conduction ABR testing using a specified staircase threshold search to establish threshold levels and Wave V peak latencies. Results Median air conduction hearing thresholds using TB-ABR ranged from 0-20 dB nHL, depending on stimulus frequency. Median bone conduction thresholds were 10 dB nHL across all frequencies, and median air-bone gaps were 0 dB across all frequencies. There was no significant threshold difference between left and right ears and no significant relationship between thresholds and hearing loss risk factors, ethnicity or gender. Older age was related to decreased latency for air conduction. Compared to previous studies, mean air conduction thresholds were found at slightly lower (better) levels, while bone conduction levels were better at 2000 Hz and higher at 500 Hz. Latency values were longer at 500 Hz than previous studies using other instrumentation. Sleep state did not affect air or bone conduction thresholds. Conclusions This study demonstrated slightly better Wave V thresholds for air conduction than previous infant studies. The differences found in the current study, while statistically significant, were within the test step size of 10 dB. This suggests that threshold responses obtained using the Kalman weighting software were within the range of other published studies using traditional signal averaging, given step-size limitations. Thresholds were not adversely affected by variable sleep states.

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“…Recently, effects of unilateral deafness have attracted clinical interest owing to the predominantly monaural therapy of prelingual deafness with one cochlear implant (Graham et al, 2009; Gordon et al, 2013) and the relatively high incidence of unilateral deafness (Eiserman et al, 2008; Watkin and Baldwin, 2012). Unilateral deafness is now considered an indication for cochlear implantation of the deaf ear, but so far mainly in cases of postlingual deafness due to tinnitus in the deaf ear (Vermeire et al, 2008; Buechner et al, 2010; Firszt et al, 2012).…”

Section: Introductionmentioning

confidence: 99%

Unilateral hearing during development: hemispheric specificity in plastic reorganizations

Kral¹,

Heid²,

Hubka³

et al. 2013

Front. Syst. Neurosci.

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The present study investigates the hemispheric contributions of neuronal reorganization following early single-sided hearing (unilateral deafness). The experiments were performed on ten cats from our colony of deaf white cats. Two were identified in early hearing screening as unilaterally congenitally deaf. The remaining eight were bilaterally congenitally deaf, unilaterally implanted at different ages with a cochlear implant. Implanted animals were chronically stimulated using a single-channel portable signal processor for two to five months. Microelectrode recordings were performed at the primary auditory cortex under stimulation at the hearing and deaf ear with bilateral cochlear implants. Local field potentials (LFPs) were compared at the cortex ipsilateral and contralateral to the hearing ear. The focus of the study was on the morphology and the onset latency of the LFPs. With respect to morphology of LFPs, pronounced hemisphere-specific effects were observed. Morphology of amplitude-normalized LFPs for stimulation of the deaf and the hearing ear was similar for responses recorded at the same hemisphere. However, when comparisons were performed between the hemispheres, the morphology was more dissimilar even though the same ear was stimulated. This demonstrates hemispheric specificity of some cortical adaptations irrespective of the ear stimulated. The results suggest a specific adaptation process at the hemisphere ipsilateral to the hearing ear, involving specific (down-regulated inhibitory) mechanisms not found in the contralateral hemisphere. Finally, onset latencies revealed that the sensitive period for the cortex ipsilateral to the hearing ear is shorter than that for the contralateral cortex. Unilateral hearing experience leads to a functionally-asymmetric brain with different neuronal reorganizations and different sensitive periods involved.

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The longitudinal follow up of a universal neonatal hearing screen: The implications for confirming deafness in childhood

Abstract: Even with UNHS in place post-neonatal routes to identification need to be maintained and improvements investigated.

Cited by 83 publications

References 32 publications

Congenital hearing loss

Congenital hearing loss

Air and Bone Conduction Click and Tone-Burst Auditory Brainstem Thresholds Using Kalman Adaptive Processing in Nonsedated Normal-Hearing Infants

Unilateral hearing during development: hemispheric specificity in plastic reorganizations

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