The diagnosis of Adamantiades-Behçet disease: Clinical features and diagnostic/classification criteria

Abstract

Adamantiades-Behçet’s disease (ABD) is a chronic-relapsing multisystemic inflammatory disease with unknown etiology first described by a Greek ophthalmology Benediktos Adamantiades and a Turkish dermatology Hulusi Behçet. Any organ or apparatus may be involved, though more often there is an involvement of oral and genital mucosae as well as ocular lesions, skin features, and vascular findings. Since there is neither laboratory nor radiological pathognomonic test, the diagnosis is basically clinical according to peculiar signs and symptoms of the disease. With the purpose of giving objectivity and homogeneity to the diagnosis, many authors in time introduced a long series of diagnostic and classification criteria for Adamantiades-Behçet’s disease. This mini-review provides an overview of published diagnostic/classification criteria.

Behçet’s disease detecting by hemoptysis and recurrent epididymo-orchitis: A case report from Syria

“…In this case, the patient exhibited recurrent oral ulcers, genital ulcers, and vascular manifestations, fulfilling the required clinical criteria for BD with a total score of 5 points. 4 BD is believed to be a vascular disorder that can manifest as occlusive lesions in veins or arteries and can also present as arterial aneurysms. These lesions are thought to be caused by perivascular or endovascular inflammation.…”

“…However, in our case, we have adopted the new International Criteria for BD, which enables physicians to diagnose the disease early. 4 In this article, we present a special case of BD involving a pulmonary artery aneurysm (PAAs). The patient exhibited symptoms such as productive cough, hemoptysis, fever, and weight loss over a period of 4 months.…”