The computed tomographic appearances in pulmonary artery atresia

Harris, Kevin M.; Lloyd, DavidJ.; Morrissey, Brendan; Adams, H.

doi:10.1016/s0009-9260(05)80995-x

Cited by 13 publications

(12 citation statements)

References 9 publications

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“…It can also provide information on pulmonary hypertension, collateral circulation and congenital cardiovascular anomalies. 9 The diagnosis of UAPA can be confirmed by ventilation-perfusion imaging. Although the usual description of the nuclear ventilation-perfusion scan in UAPA is no perfusion with intact ventilation, diminished ventilation in UAPA has also been reported confirming our observation.…”

Section: Discussionmentioning

confidence: 99%

Isolated Unilateral Pulmonary Artery Agenesis: Report of Two Cases

Bai¹,

Vishnukanth²,

Dwivedi³

et al. 2022

The Indian Journal of Chest Diseases and Allied Sciences

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Unilateral agenesis of pulmonary artery (UAPA) is a rare congenital anomaly that occurs due to malformation of the sixth aortic arch and about 70% of the patients have associated cardiovascular anomalies. However, UAPA without any associated cardiovascular anomalies is termed isolated UAPA. Cases of isolated UAPA may remain asymptomatic and survive into adulthood. Majority of the adults are asymptomatic and can present with recurrent respiratory tract infections. Presence of pulmonary hypertension carries a poor prognosis. There is no specific treatment for UAPA. We report two patients of UAPA with adult presentation.

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Section: Discussionmentioning

confidence: 99%

Isolated Unilateral Pulmonary Artery Agenesis: Report of Two Cases

Bai¹,

Vishnukanth²,

Dwivedi³

et al. 2022

The Indian Journal of Chest Diseases and Allied Sciences

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“…Confirmation and anatomical details (i.e. presence of collateral arteries, pulmonary hypertension, great vessel abnormalities, cardiac malformations and parenchymal lung diseases) can be discerned by computed tomography, magnetic resonance imaging and scintigraphy (2,8,9,10,11). Unilateral absence of pulmonary artery is usually diagnosed and surgically treated in the first year of life if it is accompanied to cardiovascular malformations (1).…”

Section: Literature Review and Discussionmentioning

confidence: 99%

“…Perfusion scintigraphy has been performed to some of these cases and authors mentioned about the importance of this technique for diagnosis of this anomaly (14,16). Ventilation-perfusion studies in pulmonary agenesis are typically described as showing no perfusion on the affected side with intact or diminished ventilation (9,11,18). Although they are slightly decreased, perfusion and ventilation are intact in pulmonary hypoplasia as the differential diagnosis (7).…”

Section: Literature Review and Discussionmentioning

confidence: 99%

Isolated Left Pulmonary Artery Agenesis: A Case Report

Balcı

Koç²,

Kırkıl³

et al. 2012

MIRT

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Unilateral pulmonary artery agenesis without any cardiovascular malformation is a rare anomaly. We present the imaging findings of a patient who was diagnosed as isolated left pulmonary artery agenesis. A 27-year-old female patient was admitted to our hospital due to dyspnea during exercise for five years. Chest X-ray revealed minimally small left pulmonary hilum and left lung. She was admitted to our clinic with the suspicion of pulmonary artery pathology. Absent perfusion of the left lung with normal ventilation was visualized on scintigraphy. MDCT angiography of pulmonary arteries showed absent left main pulmonary artery with systemic collaterals around left hemithorax. Pulmonary artery agenesis can be asymptomatic and isolated until adulthood. Both scintigraphy and CT angiography images of pulmonary artery agenesis of a patient are rare in the literature. Pulmonary ventilation-perfusion scintigraphy can be used not only for pulmonary embolism but also pathologies involving pulmonary artery and its branches. Conflict of interest:None declared.

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“…In our case, due to atresia of left pulmonary artery, right pulmonary artery got dilated, thereby increasing blood flow to the right lung and probably making it more prone to TB. v. Radiology: Chest x-ray in unilateral pulmonary artery atresia can show decreased size of the affected hemithorax, elevation of the same sided hemidiaphragm, ipsilateral hyperlucent hemithorax, absent ipsilateral hilar shadow, features suggestive of absent affected pulmonary artery with enlarged opposite side pulmonary artery shadow and displacement of the mediastinum to the affected side [13]. The differential for these radiology findings could include massive pulmonary embolism, Swyer-James syndrome and Scimitar syndrome.…”

Section: Upaa Can Also Present With Haemoptysis In Young Patientsmentioning

confidence: 99%

Exertional dyspnea and hemoptysis in an adolescent: is it tuberculosis only?

Goel

Goyal

Kumar

2021

Monaldi Arch Chest Dis

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Unilateral pulmonary artery atresia (UPAA), commonly detected in childhood, can occasionally present in adulthood with typical symptoms of recurrent pulmonary infections, dyspnoea on exertion and hemoptysis. An 18-year-old girl presented with complaints of cough, dyspnea on exertion and hemoptysis. Chest radiograph revealed dilated pulmonary trunk, signs of left sided volume loss and cavitating lesion in left lower zone. Pulmonary CT angiography found left pulmonary artery atresia. Endobronchial lung biopsy revealed granulomatous inflammation. Diagnosis of left sided UPAA with pulmonary tuberculosis was established. She responded well to the anti-tubercular therapy. This case highlights the importance of awareness about UPAA as a possible differential for exertional dyspnea, recurrent chest infections, hemoptysis and pulmonary hypertension in adults.

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The computed tomographic appearances in pulmonary artery atresia

Cited by 13 publications

References 9 publications

Isolated Unilateral Pulmonary Artery Agenesis: Report of Two Cases

Isolated Unilateral Pulmonary Artery Agenesis: Report of Two Cases

Isolated Left Pulmonary Artery Agenesis: A Case Report

Exertional dyspnea and hemoptysis in an adolescent: is it tuberculosis only?

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