The Clinical Characterization and Surgical Correction of Blepharoptosis Associated With Congenital Aniridia

Abstract

The degree of ptosis is significant, and levator function is typically reduced. Ocular surface viability appears to play a key role in preoperative, intraoperative, and postoperative management. While we are aware that congenital aniridia is rather rare, we believe these recommendations are generalizable to patients with severe ocular surface disease.

Protocole national de diagnostic et de soins (PNDS) de l’aniridie congénitale : synthèse pour le médecin traitant

“…Les ptosis sévères de la paupière supérieure peuvent bénéficier d'une chirurgie de suspension frontale pour améliorer le champ visuel et dégager l'axe optique. Il n'y a pas en général d'indication du traitement chez les enfants, [Peralta et al, 2015]. Les indications chirurgicales sont restreintes aux ptosis sévères de l'adulte.…”

Congenital aniridia: etiology, manifestations and management

“…Surgical management of ptosis in this subset of patients needs a careful approach according to guidelines in a report recently published for ptosis surgery in aniridic patients [70]. …”