The Budd-Chiari Syndrome in a Child: A Case Report and Review of the Literature

Abstract

The Budd-Chiari Syndrome is associated with hepatic venous outflow obstruction. This syndrome is rare in infants and children. As this syndrome is uncommon, especially in the paediatric age group, misdiagnoses and delays in the diagnosis are frequent. A high index of clinical suspicion along with a radiological aid and a histopathological correlation can lead to an early diagnosis and an appropriate management in such cases.This case report highlights the occurrence of this rare condition in the paediatric age group as well as it redefines the salient features of this syndrome.

Living donor liver transplantation on pediatric patient with Budd-Chiari syndrome: Case report and literature review

“…It is suspected that the cause of Budd–Chiari syndrome in this patient's case is membranous obstruction, which is consistent with the profile of patients with Budd–Chiari syndrome in Asian populations [ 9 , 10 ]. Similar to the study by Misra et al [ 11 ], the etiology of membranous obstruction remains idiopathic. On the basis of the liver biopsy results of this case, the fibrosis in the portal area and confluent necrosis caused by vascular disorders were evident, supporting the suspicious of the presence of thrombosis.…”

A benign psoas teratoma of the non‐pelvic retroperitoneal space: A case report

“…Since many teratomas are resistant to chemotherapy it is not surprising that it was still present in the donor (Foster et al, 1996). We could find scarce examples of a teratoma being associated with bladder cancer, and what was found only mentioned malignant teratomas (Misra et al, 1997). The presence of a retroperitoneal benign cystic teratoma in an individual with metastatic bladder cancer may represent a unique finding not previously mentioned in the literature.…”

Pediatric Budd-Chiari Syndrome Secondary to Antiphospholipid Syndrome Running Title: Pediatric Budd-Chiari Syndrome

“…The probable associated etiologies include prothrombotic states, oncological, infectious, autoimmune or intrinsic coagulation defects. BCS can be observed at any age, but is uncommon in children and only 5% were found to be below 12 years of age [7]. The diagnosis is established by demonstrating obstruction of the venous outflow and structural changes of the liver, portal or venous system.…”