Test and teach: Ill-defined subendocardial nodules in an infant Part 1

Cardiac tumours in infancy

“…Histiocytoid cardiomyopathy also known as oncocytic cardiomyopathy, Purkinje cell tumour, focal lipid cardiomyopathy and idiopathic infantile cardiomyopathy 51 are rare arrhythmogenic disorders and are essentially hamartomatous proliferation of cardiac cells with oncocytic features. 6 The most common clinical presentation is with arrhythmias such as paroxysmal atrial tachycardia, atrial fibrillation, ventricular fibrillation, ventricular tachycardia and junctional tachycardia 52 and may even lead to sudden unexpected death in infancy.…”