AH Al-Salem, A Al-Faraj, V Talwalker, Congenital Rectal Stenosis: A Simple Approach to Management. 1994; 14(1): 56-57 Rectal atresia is a rare type of high anorectal malformation and of the variants of rectal atresia, congenital rectal stenosis is the least common type.1 Various surgical procedures 2-5 have been described for the management of rectal atresia, but due to its rarity, there is no standard tested approach for its management. We present a case of congenital rectal stenosis in a 3-1/2-year-old female and describe a simple technique for its management.
Case ReportA 3-1/2-year-old female was referred to Qatif Central Hospital because of soiling her pants with liquid stools since birth, and just prior to her presentation, she started to complain of abdominal pain and distention. On examination, she was found to have mild abdominal distention with palpable fecal masses in the abdomen. A hard fecaloma was palpated in the pelvis on rectal examination, while the rectum was empty. After repeated rectal washouts, it was noted that the fecaloma was in the proximal part of the rectum immediately above a diaphragm with a central hole about 3 cm from the dentate line. This was confirmed by a barium enema (Figures 1 and 2).
Surgical TechniqueThe patient underwent a laparotomy through a transverse suprapubic incision. The upper third of the rectum and sigmoid colon were dilated and hypertrophied, while the lower part of the rectum was normal in caliber and the junction between the two was clearly seen. There was no other pathology. The sigmoid colon was opened longitudinally to visualize the septum, which had a central hole. The #28 EEA gun (without anvil) was introduced transanally. The shaft was guided into the opening by a finger into the proximal rectum, through the opening in the sigmoid colon. The anvil was screwed on the shaft through the colotomy opening until it was flush at the site of the central hole. The gun was then fired. The head was released and the entire instrument was recovered from the anus (Figures 3a, b, and c). The gun contained a complete disc of tissue with a central opening. The integrity of the anastomosis was confirmed and the opening in the sigmoid colon was closed longitudinally in two layers.