Systematic review of inferior vena cava atresia

Saab, Karim; Brahmandam, Anand; Brackett, Alexandria; Desai, Mayur M.; Dardik, Alan; Guzman, Raul J.; Chaar, Cassius Iyad Ochoa

doi:10.1016/j.jvsv.2023.07.002

Cited by 4 publications

(6 citation statements)

References 73 publications

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“…Surgical interventions, including open venous reconstruction or EVR, may be warranted in those patients with severe symptoms refractory to other treatments. 1,4 With supportive imaging from high-quality CT at the time of initial evaluation and invasive venography at the time of intervention as well as the advancement of endovascular reentry devices, endovascular reconstruction has become possible. 7 Approximately 13% of patients with IVC atresia will undergo EVR.…”

Section: Discussionmentioning

confidence: 99%

“…7 Approximately 13% of patients with IVC atresia will undergo EVR. 1 Despite the potential for significant symptom improvement and the suggested safety outcomes in published literature, careful case selection is needed due to the complexity and heterogeneity of the anatomy in cases of IVC atresia. 1,6 EVR is thought to be feasible in any case in which a wire can be safely passed across the atretic segment of the IVC.…”

Section: Discussionmentioning

confidence: 99%

“…IVC atresia, on the other hand, is due to a partial failure of proper development of any of the primordial veins or a secondary process such as IVC thrombosis that leads to a significant reduction in the IVC lumen. 1 In these conditions, deoxygenated blood returns to the right atrium through a robust collateral venous system. 2 IVC atresia is a rare condition with a prevalence of 0.0005%-1% of the population.…”

Section: Introductionmentioning

confidence: 99%

“…2 IVC atresia is a rare condition with a prevalence of 0.0005%-1% of the population. 1,2 It can be asymptomatic due to collateral flow and discovered incidentally in approximately 25%-33% of cases. 1,3 However, patients may present with a myriad of symptoms such as painful engorgement of superficial collateral veins, lower extremity swelling, venous thrombosis (VT) at a young age, non-healing venous ulcers, and rarely renal dysfunction.…”

Section: Introductionmentioning

confidence: 99%

“…1,2 It can be asymptomatic due to collateral flow and discovered incidentally in approximately 25%-33% of cases. 1,3 However, patients may present with a myriad of symptoms such as painful engorgement of superficial collateral veins, lower extremity swelling, venous thrombosis (VT) at a young age, non-healing venous ulcers, and rarely renal dysfunction. Premature development of lower extremity VT is the most common initial presentation of this condition.…”

Section: Introductionmentioning

confidence: 99%

See 4 more Smart Citations

Multimodal imaging assessment for feasibility of endovascular reconstruction in cases of inferior vena cava atresia

Kisling,

Basile,

Dagher

et al. 2024

Clinical Case Reports

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

See 3 more Smart Citations

Multimodal imaging assessment for feasibility of endovascular reconstruction in cases of inferior vena cava atresia

Kisling,

Basile,

Dagher

et al. 2024

Clinical Case Reports

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Unveiling absent inferor vena cava in young patients: Case reports and clinical insights

Tadayon,

Najari,

Refaei

et al. 2024

International Journal of Surgery Case Reports

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KILT Syndrome: A Systematic and Historical Review

2023

JMCCR

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Background: Kidney and IVC Abnormalities with Leg Thrombosis (KILT) is a rare condition that affects young individuals. It involves a clinical triad that consists of deep vein thrombosis of the legs, usually caused by a congenital abnormality of the inferior vena cava (IVC) that, in turns, leads to venous stasis, with the third component, also incidental, being the presence of unilateral renal agenesis. Aims: A systematic review is conducted of the literature to understand the syndrome’s current state from the following perspectives: a) clinical (presentation, diagnosis, and treatment), b) historical (before-and-after of the KILT acronym), and c) critical (evaluation of the syndrome’s three components). Methods: A systematic review using PRISMA methodology to identify the observational studies published in PubMed/Medline and Wiley/Cochrane Library that describe cases of KILT syndrome. The search concluded on December 15, 2023. Results: The search produced 620 potential publications. Following the removal of duplicates, non-relevant studies, and appropriate screening, the final sample consisted of 27 studies covering 29 cases of KILT (19 males, eight females, and four non-defined, aged 29.8 ± 2.7 years at the time of the diagnosis). A descriptive analysis of their characteristics is provided. Conclusions: KILT syndrome is an uncommon disorder, and the conclusions are based on a limited literature sample. Most of the cases share the symptoms of painful edema on the legs, the iliac location of the thrombosis, and the incidental diagnosis of full or partial agenesis of the IVC (with the appearance of collateral venous pathways) and renal hypoplasia with hypertrophy of the contralateral kidney. The diagnosis is based on imaging scans, and the long-term use of anticoagulants is the main form of treatment. The dearth of case studies limits a more precise understanding of recurrent thrombotic episodes and the post-thrombotic syndrome.

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Systematic review of inferior vena cava atresia

Cited by 4 publications

References 73 publications

Multimodal imaging assessment for feasibility of endovascular reconstruction in cases of inferior vena cava atresia

Multimodal imaging assessment for feasibility of endovascular reconstruction in cases of inferior vena cava atresia

Unveiling absent inferor vena cava in young patients: Case reports and clinical insights

KILT Syndrome: A Systematic and Historical Review

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