Syringo-Encephalomyelia

Kirgis, Homer D.; Echols, Dean H.

doi:10.3171/jns.1949.6.5.0368

Cited by 23 publications

(6 citation statements)

References 3 publications

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“…Syringobulbia in isolation has been described. [5][6][7] There is a long established tradition for regarding syringobulbia as a "developmental" lesion with the inference that it may be related to dysraphism. This attitude was taken by pathologists working in an era before modern imaging and surgery.…”

Section: Discussionmentioning

confidence: 99%

Syringobulbia: a surgical appraisal.

Morgan¹,

Williams²

1992

Journal of Neurology, Neurosurgery & Psychiatry

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Syringobulbia is a term which has been clinically applied to brain stem symptoms or signs in patients with syringomyelia. Syringobulbia clefts are found on investigation or at necropsy caused by cutting outwards of the CSF under pressure from the fourth ventricle into the medulla. Hindbrain hernia headache has not been used on its own as a selection criterion neither has syncope nor nystagmus. There were 34 females and 20 males. Forty four patients were available for review. Of the remainder, two had died of unrelated causes and 8 were untraceable or lived an excessive distance away. The age at diagnosis for females was 10-58, a mean of 37-3, and males 18-61, a mean of 44. The symptoms often started many years before diagnosis. The mean follow up period from the original operation was 14-2 years, range 3-39. Thirty four patients had either radiological or clinical evidence of syringomyelia, 20 cases had hindbrain features without syringomnyelia.Skull radiographs show basilar impression in 26 cases and CT scanning and myelography or MRI showed that 46 had tonsillar descent, 28 had a demonstrable syrinx in the spine. Two did not undergo CT scanning, myelography or MRI.All patients had CVD. The technique included a small craniectomy decompressing the tonsils usually by removing the arachnoid and often by sucking away part of the tissue of the tonsils, and always stitching the dura back and leaving it widely open. Five patients had ventriculo-atrial shunting (VEA) following postoperative deterioration, one of these had a syringopleural shunt at the time of the CVD and two had late syringopleural shunting.At review each patient completed a questionnaire and had a neurological and otolaryngological (ENT) examination.

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Section: Discussionmentioning

confidence: 99%

Syringobulbia: a surgical appraisal.

Morgan¹,

Williams²

1992

Journal of Neurology, Neurosurgery & Psychiatry

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“…The majority of these publications on hydrosyringomyelia in childhood do not indicate whether enclosed or communicating forms are involved. I t can be seen only from the case description of Duffy and Ziter (1964), Huebert and Mac Kinnon (1969) and Kirgis and Echols 1949) that the syrinx cavities in the four children observed did not communicate with the ventricular system.…”

Section: Age At Onsetmentioning

confidence: 88%

“…Whereas in adults, dissociated disorder of sensation is the most frequent symptonl detected in an early stage of the disease (23,26,34,42), it can only be detected in older children who cooperate in a sensitivity examination. In children, pain in the back, head or abdomen is often the first subjective manifestation of the disease (21,22,26,29,43).…”

Section: Clinical Symptomatologymentioning

confidence: 99%

Hydrosyringomyelia in Childhood Clinical Aspects, Pathogenesis and Therapy

Eggers¹,

Hamer²

1979

Neuropediatrics

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“…[ 14 ] Lastly, an argument that at some point in development, the ventricular wall ruptured to allow (CSF) to dissect into the adjacent brain parenchyma in a manner similar to the extension of CSF from the central canal into the spinal cord to form a syrinx. [ 8 14 ]…”

Section: Discussionmentioning

confidence: 99%

Posterior fossa giant tumefactive perivascular spaces: 8-year follow-up in an adolescent

et al. 2015

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Background:Cystic masses in the posterior fossa are ominous appearing lesions with broad differential diagnosis. Giant tumefactive perivascular spaces (GTPS) are rarely occurring pathological findings in the posterior fossa with unclear etiology and ill-defined long-term prognosis.Case Description:We present a case of a 15-year-old male diagnosed with posterior fossa GTPS. The patient remained asymptomatic during the 8-year follow-up after diagnosis with the serial magnetic resonance imaging (MRI) showing no change in the size and morphology of the lesion.Conclusion:This case supports prior literature on supratentorial GTPS suggesting that the natural history of GTPS is mostly benign. Identification of GTPS in the posterior fossa could prevent the patient from unnecessary surgery or other aggressive treatment modalities.

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Syringo-Encephalomyelia

Cited by 23 publications

References 3 publications

Syringobulbia: a surgical appraisal.

Syringobulbia: a surgical appraisal.

Hydrosyringomyelia in Childhood Clinical Aspects, Pathogenesis and Therapy

Posterior fossa giant tumefactive perivascular spaces: 8-year follow-up in an adolescent

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