“…2,5,6,[8][9][10][11][12] The clinical features of the disease are still unclear. Table 1 summarizes the clinical features, diagnoses, and surgical strategies of the 9 cases (including our case).…”
Section: Discussionmentioning
confidence: 99%
“…Various surgical approaches have been adopted such as the pre-auricular approach combined with middle fossa craniotomy, trans-zygomatic craniotomy, and others. 2,5,6,[8][9][10][11][12] One patient underwent two-staged surgery. As the intracranial mass arising from the TMJ is located in the temporal base, extensive exposure of the temporal skull base is beneficial for total removal of the intracranial mass.…”
A 52-year-old man presented with an extremely rare case of synovial chondromatosis in the temporomandibular joint (TMJ) with extension into the middle cranial fossa manifesting as swelling and exacerbation of pain. He had a long history of right TMJ disorders. Computed tomography and magnetic resonance imaging showed a mass in the right TMJ with extension into the intracranial part through the destroyed temporal skull base. The preoperative diagnosis was chondrosarcoma or osteosarcoma. The patient underwent surgery via combined trans-zygomatic temporal skull base and pre-auricular approaches and the mass was totally removed. Histological examination found an enormous number of closely packed loose bodies of various sizes, consisting of hyaline chondrocytes. The histological diagnosis was synovial chondromatosis. This rare lesion is difficult to discriminate from chondrosarcoma, so total removal is essential for correct diagnosis and cure.
“…2,5,6,[8][9][10][11][12] The clinical features of the disease are still unclear. Table 1 summarizes the clinical features, diagnoses, and surgical strategies of the 9 cases (including our case).…”
Section: Discussionmentioning
confidence: 99%
“…Various surgical approaches have been adopted such as the pre-auricular approach combined with middle fossa craniotomy, trans-zygomatic craniotomy, and others. 2,5,6,[8][9][10][11][12] One patient underwent two-staged surgery. As the intracranial mass arising from the TMJ is located in the temporal base, extensive exposure of the temporal skull base is beneficial for total removal of the intracranial mass.…”
A 52-year-old man presented with an extremely rare case of synovial chondromatosis in the temporomandibular joint (TMJ) with extension into the middle cranial fossa manifesting as swelling and exacerbation of pain. He had a long history of right TMJ disorders. Computed tomography and magnetic resonance imaging showed a mass in the right TMJ with extension into the intracranial part through the destroyed temporal skull base. The preoperative diagnosis was chondrosarcoma or osteosarcoma. The patient underwent surgery via combined trans-zygomatic temporal skull base and pre-auricular approaches and the mass was totally removed. Histological examination found an enormous number of closely packed loose bodies of various sizes, consisting of hyaline chondrocytes. The histological diagnosis was synovial chondromatosis. This rare lesion is difficult to discriminate from chondrosarcoma, so total removal is essential for correct diagnosis and cure.
“…Pijn en zwelling in de regio van het aangedane gewricht zijn echter de meest voorkomende symptomen (Von Lindern et al, 2002;Holmlund et al, 2003;Guarda-Nardini et al, 2010). In die gevallen waarbij de aandoening zich uitstrekt naar de fossa infratemporale, naar de fossa pterygopalatina of naar de porus acusticus externus, kunnen neurologische problemen ontstaan, bijvoorbeeld verandering van smaak, duizeligheid, gehoorverlies, tinnitus en paralyse van de nervus facialis (Rosati en Stevens, 1990;Sun et al, 1990;Acar et al, 2007;Lieger et al, 2007;Xu et al, 2007).…”
Wat is nieuw?Een klinisch kenmerk van synoviale chondromatose van het temporomandibulaire gewricht dat niet typerend is voor temporomandibulaire disfunctie, is een vaste, stugge, niet fluctuerende zwelling om de laterale pool van het gewricht.
PraktijktoepassingSynoviale chondromatose dient te worden overwogen bij de differentiële diagnostiek van patiënten met temporomandibulaire disfunctieklachten. Palpatie en röngtendiagnostiek kunnen de afwijking opsporen.
“…6 Hay pacientes con una historia de larga evolución en los que la CS tiene un comportamiento localmente destructivo, con erosión de la fosa glenoidea o infratemporal y extensión hacia la fosa cerebral media; aunque se mantiene extradural, se han descrito erosiones óseas masivas, con desplazamiento de estructuras y parálisis del nervio facial. 7,9,11,12,15 En estas situaciones el diagnóstico diferencial debe realizarse con procesos neoplásicos. Se debe asegurar el control local y la exéresis completa que permita su análisis posterior, para descartar malignidad, y evitar el riesgo de degeneración de la lesión residual.…”
Section: Which Makes Diagnosis Difficultunclassified
“…Although it may remain extradural, massive bone erosion has been described, with displacement of structures and paralysis of the facial nerve. 7,9,11,12,15 In this situation the differential diagnosis should be carried out with neoplastic processes. Local control should be ensured, together with complete exeresis enabling posterior analysis so as to rule out malignancy, and in order to avoid the risk of degeneration of the residual lesion.…”
Section: Which Makes Diagnosis Difficultmentioning
Resumen: La afectación de la ATM por una condromatosis sinovial es un hecho muy poco frecuente. Trastorno metaplásico del tejido sinovial, suele producir cuerpos libres, condromas, intraarticulares. Tiene una clínica variable y muy inespecífica. Las pruebas diagnósticas de elección son la RM y la artroscopia. La retirada de cuerpos libres y sinovectomía parcial suele ser terapéutica. Ocasionalmente puede destruir la base del cráneo y extenderse intracranealmente. Se han descrito casos de malignización secundaria. Es necesario el seguimiento a largo plazo del paciente. Presentamos un caso con osteolisis incipiente de la fosa cerebral media.Abstract: Synovial chondromatosis very rarely affects the TMJ. It is a metaplastic disorder of the synovial tissue that usually produces intra-articular loose bodies, or chondromas. It has variable clinical features and the symptoms are unspecific. Examination by means of magnetic resonance imaging and arthroscopic observation are the diagnostic techniques of choice. Treatment consists in the removal the loose bodies and partial synovectomy. Occasionally the skull has been destroyed and the middle cranial fossa invaded. There are cases of malignant transformation to chondrosarcoma. A long-term follow up is necessary. We describe a case with incipient intracranial extension.
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