Syndrome de Susac

Papo, Thomas; Klein, Isabelle; Sacré, Karim; Doan, Serge; Bodaghi, Bahram; Aubart-Cohen, F.

doi:10.1016/j.revmed.2011.11.002

Cited by 15 publications

(4 citation statements)

References 21 publications

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“…Susac’s syndrome is probably caused by the obstruction of pre-capillary arterioles of the brain, retina and inner ear, secondary to lesions from anti-endothelial cell antibodies [ 50 ]. The physiopathology of the selective tissue distribution is still not clearly understood; this could be explained by a common embryologic origin of the brain [ 51 ]. Symptoms include visual and hearing disturbances, as well as neurological deficits, the latter mimicking stroke or transient ischaemic attacks.…”

Section: Stroke Mimics With Abnormal Dwimentioning

confidence: 99%

Magnetic resonance imaging of arterial stroke mimics: a pictorial review

et al. 2018

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Acute ischaemic stroke represents the most common cause of new sudden neurological deficit, but other diseases mimicking stroke happen in about one-third of the cases. Magnetic resonance imaging (MRI) is the best technique to identify those ‘stroke mimics’. In this article, we propose a diagnostic approach of those stroke mimics on MRI according to an algorithm based on diffusion-weighted imaging (DWI), which can be abnormal or normal, followed by the results of other common additional MRI sequences, such as T2 with gradient recalled echo weighted imaging (T2-GRE) and fluid-attenuated inversion recovery (FLAIR). Analysis of the signal intensity of the parenchyma, the intracranial arteries and, overall, of the veins, is crucial on T2-GRE, while anatomic distribution of the parenchymal lesions is essential on FLAIR. Among stroke mimics with abnormal DWI, T2-GRE demonstrates obvious abnormalities in case of intracerebral haemorrhage or cerebral amyloid angiopathy, but this sequence also allows to propose alternative diagnoses when DWI is negative, such as in migraine aura or headaches with associated neurological deficits and lymphocytosis (HaNDL), in which cortical venous prominence is observed at the acute phase on T2-GRE. FLAIR is also of major interest when DWI is positive by better showing evocative distribution of cerebral lesions in case of seizure (involving the hippocampus, pulvinar and cortex), hypoglycaemia (bilateral lesions in the posterior limb of the internal capsules, corona radiata, striata or splenium of the corpus callosum) or in posterior reversible encephalopathy syndrome (PRES). Other real stroke mimics such as mitochondrial myopathy, encephalopathy, lactic acidosis, stroke-like episodes (MELAS), Susac’s syndrome, brain tumour, demyelinating diseases and herpes simplex encephalitis are also included in our detailed and practical algorithm.Key points • About 30% of sudden neurological deficits are due to non-ischaemic causes. • MRI is the best technique to identify stroke mimics. • Our practical illustrated algorithm based on DWI helps to recognise stroke mimics.

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Section: Stroke Mimics With Abnormal Dwimentioning

confidence: 99%

Magnetic resonance imaging of arterial stroke mimics: a pictorial review

et al. 2018

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“…However, the delay to realize MRI was important, as abnormalities might appear during the course of the disease. Audiogram revealed severe bilateral deafness, according to the literature [4]. Electroencephalogram was often disturbed by Susac syndrome with encephalopathy, revealing diffuse brain suffering [5].…”

Section: Discussionmentioning

confidence: 99%

Susac syndrome: about two cases

Bâ¹,

Ba²,

Guèye³

et al. 2019

Pan Afr Med J

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“…69,70 On MRI, Leptomeningeal enhancement, and lesions in basal ganglia, frequently occurs and can be a clue to diagnosis. 71 Fluorescein angiography is used for diagnosis of retinal artery branch occlusion. 72 The main differential diagnoses are demyelinating conditions (MS, ADEM, and MOGAD), infarction (vasculitis and thromboembolic disease), and infection.…”

Section: Susac Syndromementioning

confidence: 99%

Autoimmune disease of head and neck, imaging, and clinical review

et al. 2022

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Autoimmune disease of the head and neck (H&N) could be primary or secondary to systemic diseases, medications, or malignancies. Immune-mediated diseases of the H&N are not common in daily practice of radiologists; the diagnosis is frequently delayed because of the non-specific initial presentation and lack of familiarity with some of the specific imaging and clinical features. In this review, we aim to provide a practical diagnostic approach based on the specific radiological findings for each disease. We hope that our review will help radiologists expand their understanding of the spectrum of the discussed disease entities, help them narrow the differential diagnosis, and avoid unnecessary tissue biopsy when appropriate based on the specific clinical scenarios.

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Syndrome de Susac

Cited by 15 publications

References 21 publications

Magnetic resonance imaging of arterial stroke mimics: a pictorial review

Magnetic resonance imaging of arterial stroke mimics: a pictorial review

Susac syndrome: about two cases

Autoimmune disease of head and neck, imaging, and clinical review

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