Symptomatic Double Aortic Arch Causing Tracheal and Esophageal Compression in the Adult

The Presentation of a Double Aortic Arch in Adulthood in Association with Congestive Heart Failure Attributed to a Previously Silent Aortic Regurgitation

“…Symptomatic cases that manifested themselves for the first time in adulhood have been reported much less frequently [2,4], Some of these cases were most likely overlooked because of an unawareness of this malforma tion or they were misdiagnosed as other diseases even when they were symptomatic; this is what occurred the first time when symptoms appeared in the present case. It is very important to be aware of this condition for a cor rect diagnosis [1,4], Cardiovascular lesions were rarely associated with DAA but included tetralogy of Fallot [5], transposition of great arteries [5], ventricular septal defect [7], patent duc tus arteriosus [7] and traumatic rupture of the retro esophageal arch [8]. To our knowledge, the association of AR with DAA has not been previously reported, and it was not clear whether the association of AR in this case was incidental.…”

“…The incidence and fate of persons who have an asymp tomatic double aortic arch (DAA) have not been well doc umented [1,2], In general, DAA presents the symptoms earlier in life compared to other types of vascular rings [ 1,3], and the late presentation of the condition in adulthood is uncommon [2,4], This paper describes an adult case of DAA (Edwards type IA [5]). The patient had been asymp tomatic for DAA but presented difficulty in swallowing in association with congestive heart failure attributed to a previously silent aortic regurgitation (AR).…”

Persistent Fifth Aortic Arch Associated with Coarctation of Aorta: A Case Report

“…Persistent fifth aortic arch is a rare anomaly in which both arches pass the trachea anteriorly in contrast to double aortic arch, in which both arches surround the tracheoesophageal axis and may cause dysphagia or respiratory distress 5 …”

“…Persistent fifth aortic arch is a rare anomaly in which both arches pass the trachea anteriorly in contrast to double aortic arch, in which both arches surround the tracheoesophageal axis and may cause dysphagia or respiratory distress. 5 Embryologically, persistent fifth aortic arch stems from the persistence of the fifth arch of the branchial arch system. This arch usually regresses very early in human embryos.…”

Doppelter Aortenbogen Klinik, Diagnose und Therapie bei Kindern und Erwachsenen

“…In der Literatur sind weniger als 25 Patienten beschrieben, einige waren bis ins hohe Alter komplett asymptomatisch (8-11, 14, 17, 18, 26, 29, 30). Wenn der vaskuläre Schnürring nur eine geringe Kompression der Trachea und Ösophagus verursacht, werden die typischen Symptome des doppelten Aortenbogens möglicherweise durch nicht spezifische respiratorische Beschwerden maskiert und die richtige Diagnose wird über Jahre hinweg verfehlt (10,11,18,19).…”