Swollen digits due to pachydermodactyly resembling inflammatory arthritis

Abstract

Pachydermodactyly is a rare digital fibromatosis, characterized by painless, fusiform swelling in proximal interphalangeal joints. Since it may be misdiagnosed as inflammatory arthritis, it is important to call physicians’ attention to this rarely seen condition to avoid unnecessary immunosuppressive treatment. Hereby, we present a case of a pachydermodactyly that had been previously followed-up and treated as an inflammatory arthritis for 4 years. We describe the clinical, radiological, and dermoscopic features of the case.

Pachydermodactyly

“…Mucin deposition was noted in the dermis (figure 2A,B). Pachydermodactyly is a rare benign digital fibromatosis 1. It usually starts in puberty and female to male ratio is 1.0:3.9 2.…”