Surgical treatment of Servelle-Martorell syndrome

Abstract

Servelle-Martorell sendromu, etyolojisi ve prognozu tam olarak bilinmemesine karşın, tutulan ekstremitenin yumuşak doku hipertrofisi ve kas-iskelet sistemi hipotrofisi ile karakterize, genellikle venöz, ancak nadiren arteriyel vasküler malformasyonudur. Genellikle vasküler malformasyonların tedavisinde cerrahi kısıtlı şartlarda uygulanmakla birlikte, komplikasyon gelişiminde kaçınılmazdır. Bu vasküler malformasyonlar sıklıkla kompresyon çorabı ve ilaçlar ile medikal olarak tedavi edilir. Bu yazıda, venöz malformasyon nedeniyle cerrahi olarak tedavi edilen 20 yaşında bir Servelle-Martorell sendromlu erkek olgu sunuldu.

Servelle-Martorell syndrome in an adult: A case report with findings on CT angiography

“…Surgery is rarely performed unless there are complications, such as aneurysms or severe shunts. Establishing decisions for surgical intervention must be based on multiple consultations and careful preparation [3] . In some cases, excision of localized telangiectatic veins can be effective if the deep vein system has good function.…”

“…This syndrome is characterised by sinuous dilatation of superficial veins and bony hypoplasia, causing limb hypertrophy, usually of the upper limb; therefore, it is also known as angiodysplasia-osteohypotrophic syndrome. There are many different treatment methods, including conservative ones [3] . Servelle-Martorell syndrome has rarely been reported in the literature.…”

“…Servelle-Martorell syndrome has rarely been reported in the literature. There are no studies with a sample size large enough to assess the prognosis [1] , [2] , [3] , [4] .…”