We report a case of a rare schwannoma of the jugular foramen and removed it by a limited transjugular approach. A limited surgical approach was performed for removal of the tumour, with preservation of surrounding structures. A thorough understanding of the anatomy of the region is necessary for our limited transjugular approach. The schwannoma was successfully removed. Through a detailed understanding of the anatomy of the region and adequate classification of the tumour, a limited surgical approach is not only possible, but preferable.