Key wordsaorto-right atrial tunnel, aorto-right atrial communication, tricuspid atresia.Aorto-right atrial communication is an uncommon heart defect, and this malformation could be generally caused from ruptured aneurysm of sinus Valsalva, ruptured dissecting aneurysm of the ascending aorta, and coronary artery fistula. [1][2][3][4] Here, we report on a distinctly unique case of aorto-right atrial shunt that is associated with aortic atresia, tricuspid atresia, ventricular septal defect, atrial septal defect, and persistent ductus arteriosus.