Coronary artery fistulae (CAF) are a rare entity describing abnormal communication between a coronary artery and cardiac chamber or a large intrathoracic vessel and are seldom described in the literature . These fistulae can be either congenital or acquired. Often incidental in finding, CAFs can have serious clinical sequelae, and should be duly reported and discussed with the cardiac team. More than 50% of patients with CAFs may be asymptomatic; 34% may report chest pain; 13% may have symptoms of heart failure, and a minority of 2% may suffer from endocarditis and arrhythmias . The largest series to our knowledge was reported by the Cleveland Clinic, which found 225 patients with incidental CAF out of 126,595 coronary catheterizations (incidence of 0.18%), performed during a span of 28 years . Multiple CAFs are an even rarer entity and only a handful of cases have been reported in the literature to date. Few cases of double CAFs have been reported that describe two different feeder coronary arteries giving rise to separate drainage sites . In our report, however, we describe a new entity: a single-feeder coronary vessel communicated with two drainage sites. Our case is curiously unique, in which we report a single artery, originating from the right coronary artery (RCA) with double drainage sites -one to the left pulmonary artery and the second to the left bronchial artery.
LEARNING POINTS• Cardiac CTA confers added value in identification of both normal and abberant coronary vessels.• Maximal Intensity Projection (MIP) & 3D volumetric reconstructions are of added value in every cardiac CTA due to its all-encompassing view of the heart. These techniques have been incorporated and are routinely used in all our Cardiac CTAs.• Curved MIP reconstructions of the coronary arteries, combined with 3D volumetric reconstruction of the heart, allows comprehensive evaluation of the coronary arteries, especially in complicated cases.• Due to its anatomic and 3-dimensional properties -not only of the heart -but of the entire thorax, cardiac CTA is ideal for evaluation of fistulae between coronary arteries and adjacent vessels.• Cardiac CTA may facilitate the illustration of single-feeder, double-drainer coronary artery fistulae, which was not clearly identified in our case during conventional coronary angiography.
KEYWORDS Coronary artery fistula, abberant coronary artery, cardiac CT, cardiac catheterization CASE PRESENTATIONA 65-year-old male with longstanding metabolic syndrome and ischemic heart disease presented to the ED with chest pain and dyspnea. Fifteen years earlier, the patient underwent coronary artery bypass, which included Left Internal Mammary Artery to Left Anterior Descending Artery (LIMA-to-LAD) and SVG-to-M1. Due to his clinical manifestation, a diagnostic angiography study was performed, and a stent was inserted into a tight stenosis of the proximal SVG. Incidentally, a tortuous vessel was revealed: it originated from the RCA, passed upward and drained into a large vessel, where a turbulent steal ...