Surgical Treatment for and Prognosis of Congenital Pulmonary Airway Malformation

Usui, Noriaki

doi:10.1007/978-981-15-5175-8_8

Cited by 1 publication

(2 citation statements)

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“…Due to the increased pulmonary vascular resistance, right to left shunting via the ductus arteriosus may have occurred, leading to hypoxemia and acidosis. Based on the pathophysiology, CPAM lesions tend to become infected due to the communication established between the normal airways and the cystic lesions [7]. Due to this communication, lesions can easily become infected by the deposition of external pathogens.…”

Section: Discussionmentioning

confidence: 99%

“…The resection should be clear of any remnants to promote the development of normal lung tissue. During surgery, the cystic lesion has the potential to become enlarged due to the influx of air from positive pressure ventilation and hence, pulmonary resection should be performed as soon as possible without further delay [7]. Some guidelines recommend performing total pneumonectomy in stages to prevent complications such as right pneumonectomy syndrome, reported in a case by Stolar et al [11].…”

Section: Discussionmentioning

confidence: 99%

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A Multi-Disciplinary Management of a Rare Case of a Complete Lung Congenital Pulmonary Airway Malformation in a Newborn from a Developing Country

Dhillon

2022

IJOPRS

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Congenital pulmonary airway malformation (CPAM) is a pulmonary malformation in which parts of the lung are replaced by hamartomatous, cystic, or non-functional abnormal tissue. Herein, we present a case of life-saving pneumonectomy in an infant with type II CPAM which affected entire right lung. A 1-day-old male infant who was a known case of CPAM presented with progressive respiratory distress requiring intubation. There is a paucity of evidence regarding the management protocol of entire lung CPAM. After multi-disciplinary input, right-sided pneumonectomy was performed. Thereafter, he had a prolonged, complicated hospital stay due to prolonged intubation, complicated by pneumonia, sepsis, and metabolic abnormalities. In this report we discuss the etiology, surgical procedure, management strategies, challenges faced in decision making of management, as well as potential complications, which make this case report a valuable asset to the scientific literature. Our case report contributes towards the scare literature present with regards to management of CPAM in the presence of respiratory distress. After receiving appropriate post-operative care, the patient was eventually discharged home in a stable condition. With the advancements in modern obstetric practice, CPAM is detected prenatally and early surgical resection of the affected area is considered the best management option in symptomatic cases of CPAM. A multidisciplinary approach with CPAM diagnosed prenatally and early surgical resection of the affected area is the gold standard evidence-based management protocol that exists.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%