Surgical Repair of a Unileaflet Mitral Valve: A Rare Congenital Abnormality and a Novel Surgical Approach

Abstract

Graphical abstract

Unileaflet Mitral Valve in Patient With Marfanoid Habitus

“…Mitral valve repair or mitral valve replacement with either a mechanical or bioprosthetic valve are the current available surgical options. 5 Our patient had an unknown type of murmur found as a child and to our knowledge was not diagnosed with a congenital heart disease. The symptomatic tachyarrhythmia along with physical examination findings of marfanoid habitus and suspicion for cardiac conduction defect suggested by right bundle branch block, which can also accompany congenital heart disease, led to cardiac workup.…”

Hypoplastic Posterior Leaflet Mitral Valve Associated with Bicuspid Aortic Valve

“… 6 This pathology has been most frequently observed in infants and children with symptomatic MR, either in isolation or in association with other cardiac lesions, with a tendency to be incompatible with life in many cases beyond the neonatal period. However, some cases have been described in adults, 3 , 7 , 8 , 9 , 10 , 11 , 12 with ages ranging between 17 and 76 years, without a relationship linked to sex; usually, these adults have mild MR and relatively preserved hemodynamic parameters. Therefore, it is known that the progression of MR over the years and the clinical symptoms that develop are the main factors that lead to diagnosis.…”

“…In this case, valve repair is always the first treatment option, as long as it is anticipated that it will be successful and long-lasting. 15 Arasaratnam and collaborators, 7 in Australia, propose a technique based on mitral posterior leaflet augmentation with collagen bioscaffold patch associated with annuloplasty with ring.…”