Surgical management of double outlet right ventricle with aortopulmonary window

Abstract

We report a case of double outlet right ventricle in combination with an aortopulmonary window in a 20-month-old patient and discuss its surgical management.

Type A interrupted aortic arch and type III aortopulmonary window with anomalous origin of the right pulmonary artery from the aorta

“…An aortopulmonary window can present as an isolated lesion or in association with other congenital abnormalities including ventricular septal defect, tetralogy of Fallot, double outlet right ventricle, and a right pulmonary artery arising from the ascending aorta . Teresa Berry was the first to describe the association of a distal aortopulmonary window, aortic origin of the right pulmonary artery, intact ventricular septum, and interruption of the aorta as a syndrome in 1981 .…”