Surgical correction of cor triatriatum sinister in the paediatric population: mid-term results in 15 cases

Abstract

CTS is a rare congenital cardiac anomaly in which the results of the corrective surgery are encouraging. Early and long-term outcomes may be variable according to the associated congenital heart defects.

Supravalvular mitral ring in a patient with Turner syndrome: A case report

“…[5] Although cor triatriatum is a rare anomaly, it can be encountered in all age groups and should be considered in the differential diagnosis with supramitral ring, as both anomalies are similar in terms of clinical signs and symptoms. [6] First described by Fisher [7] in 1902, SMR has been the subject of several studies to better understand the associated cardiac abnormalities. Collison et al [8] proposed that cardiac anomalies associated with SMR could be classified into two main categories: SMR associated with ventricular septal defect, and SMR associated with left-sided obstructive pathologies, particularly sub-aortic membrane, bicuspid aortic valve, and coarctation of the aorta.…”

Mid-Term Results of Congenital Supravalvar Mitral Ring Resection

“…Figure demonstrates the SMR and cor triatriatum with the localization of the pathology in the left atrium and their relation with the left atrial appendage. It is hypothesized that cor triatriatum develops due to the failure of embryological development of the left pulmonary vein, whereas SMR is thought to be derived from a failure of the endocardial cushions to divide completely . The fibrous ring is in close proximity to the mitral valve in SMR, whereas the obstructing membrane in cor triatriatum is located more superiorly, above the left atrial appendage.…”

“…It is hypothesized that cor triatriatum develops due to the failure of embryological development of the left pulmonary vein, whereas SMR is thought to be derived from a failure of the endocardial cushions to divide completely. 6 The fibrous ring is in close proximity to the mitral valve in SMR, whereas the obstructing membrane in cor triatriatum is located more superiorly, above the left atrial appendage. The physiological properties of SMR are similar to other obstructive pathologies seen in LA, resulting in pulmonary arterial and venous hypertension.…”

“…3 Although signs, symptoms, and clinical findings may be similar, SMR should be differentiated from cor triatriatum, where the blood flow between a proximal chamber and a distal left atrial cavity is diminished by a fibromuscular membrane dividing the atrial cavity into two separate spaces. 6 The identification of these subtypes of left ventricle inflow obstruction is important since the prognosis after surgical treatment of SMR is substantially improved. Figure 3 demonstrates the SMR and cor triatriatum with the localization of the pathology in the left atrium and their relation with the left atrial appendage.…”

Hybrid balloon dilation treatment for cor triatriatum dexter in a small breed puppy

“…Cor triatriatum is a relatively rare congenital heart disease found in humans, dogs, and cats. Cor triatriatum sinister [1] and cor triatriatum dexter [2] have been reported in humans, whereas cor triatriatum dexter [3] and cor triatriatum sinister [4] have been reported in dogs and cats, respectively. Cor triatriatum dexter occurs through a different mechanism from cor triatriatum sinister, and is believed to be caused by a persistent right sinus venosus valve [5].…”