Supratentorial Primitive Neuroectodermal Tumors

Singhal, Ash; Gul, Shahid; Steinbok, Paul

doi:10.1007/978-3-642-02874-8_37

Cited by 1 publication

(2 citation statements)

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“…Secreted catecholamines are responsible for the clinical signs and symptoms of pheochromocytomas and hypertension is the most important presenting sign. CNS‐PNET, which also develops from neural crest lineage, usually arises during the first decade of life and its prognosis is poor . The prevalence of pheochromocytoma is 2/1 000 000 in pediatric patients, and the prevalence of PNET is much less .…”

Section: Discussionmentioning

confidence: 99%

“…CNS‐PNET, which also develops from neural crest lineage, usually arises during the first decade of life and its prognosis is poor . The prevalence of pheochromocytoma is 2/1 000 000 in pediatric patients, and the prevalence of PNET is much less . Therefore, the occurrence of these tumors in the same patient is an exceedingly rare condition.…”

Section: Discussionmentioning

confidence: 99%

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Childhood pheochromocytoma in a survivor of central primitive neuroectodermal tumor

Nakano

Fujimaru

Ishii

et al. 2013

Pediatrics International

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Pheochromocytoma and central nervous system primitive neuroectodermal tumor are both neural crest-derived tumors. The former is usually benign and develops mainly in adulthood and the latter brain tumor mainly occurs in childhood and has a poor prognosis. We report a case of a 15-year-old boy who developed pheochromocytoma after more than 10 years of complete remission of central primitive neuroectodermal tumor. Thus far, there have been no reports of childhood cancer survivors who developed pheochromocytoma. This quite rare occurrence of two tumors in a single patient may imply some unidentified linkage or common genetic background.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%