Supradiaphragmatic middle aorta syndrome--MR and angiographic imaging.

Watson, Nick; Chalmers, N; Naqvi, N

doi:10.1259/bjr.71.842.9579186

Cited by 9 publications

(5 citation statements)

References 12 publications

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“…The clinical characteristics of MAS were first described in 1963 [2], with the narrowing of the subisthmal aorta (unlike the typical Takayasu-type changes of the aortic arch and Leriche-type of aortic bifurcation obliterative disease) [3].…”

Section: Introductionmentioning

confidence: 99%

Mid-aortic syndrome: long-term outcome of 36 children

et al. 2009

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The clinical characteristics and outcomes of children with mid-aortic syndrome (MAS) and the effectiveness of different therapeutic approaches in reducing hypertension are still debated. We conducted a single-centre retrospective review of the records of children with MAS over 30 years. Children with angiographic evidence of a narrowed abdominal aorta were included. Therapeutic approaches included medical management, percutaneous transluminal angioplasty and/or surgical intervention. Thirty-six children had presented at a median age of 2.7 years (10 days-10 years). Thirteen (36%) patients had associated syndromes, and 44% had been diagnosed with cerebrovascular disease. All patients had involvement of multiple arteries. The mortality rate was 8% after a median follow-up period of 4.5 (range 1.1-19.7) years. Among the children who survived, 90% had obtained a reduction in their blood pressure (BP). Of the patients, 76% had had a normal estimated glomerular filtration rate (eGFR) at the last follow-up examination. Seventeen percent (six of 36) had renal dysfunction at presentation. Although MAS is a severe and widespread disease, in most cases it can be effectively treated with a combination of medical, angioplasty and surgical interventions.

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Section: Introductionmentioning

confidence: 99%

Mid-aortic syndrome: long-term outcome of 36 children

et al. 2009

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“…The clinical characteristics of MAS were fi rst described in 1962 [4] with the narrowing of the subisthmal aorta, often with involvement of the renal and splanchnic arterial branches (unlike the typical Takayasu-type changes of the aortic arch and Lerichetype of aortic bifurcation obliterative disease) [7] . Although uncommon, accounting for approximately 0.5 -2 % of all cases of aortic narrowing [1] , MAS is an important cause of renovascular hypertension in children and adolescents.…”

Section: Discussion ▼mentioning

confidence: 99%

A 13-Year-Old Girl with Arterial Hypertension - Mid-Aortic Syndrome

Meyer¹,

Fries²,

Schäfers³

et al. 2010

Klin Padiatr

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Mid-aortic stenosis (MAS) is a rare clinical entity that is characterised by profound narrowing of the abdominal aorta. MAS usually presents with severe hypertension. Treatment modalities include antihypertensive medication, angioplasty, and surgery. If adequate treatment is initiated long-term prognosis is favourable. Here, we report on 13-year-old girl with MAS who presented to our hospital with arterial hypertension. Initial diagnostic work-up and treatment in patients with MAS are presented.

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“…In addition to the endothelial cells which provide costimulatory function, other cellular components serve as antigen-presenting cells. 4 …”

Section: Fig 1 Ct Angiogram Of Abdominal Aortamentioning

confidence: 99%