Successful stent placement for cervical artery dissection associated with the Ehlers—Danlos syndrome

Abstract

This 44-year-old man with Ehlers-Danlos syndrome (EDS) Type IV presented with hemiparesis and the Gerstmann syndrome. Left carotid artery (CA) angiography revealed a dissecting aneurysm with severe stenosis located in the common CA; the lesion was successfully treated with a stent graft. The patient's clinical course after endovascular surgery was uneventful, without occurrence of megacolon. The literature for spontaneous CA dissection in EDS Type IV cases is reviewed and points for investigation and treatment are discussed.

Acute brain ischemia as a complication of the Ehlers–Danlos syndrome, the case series

“…Special attention should be paid to aortic procedures following the aortic dissection and/or aneurysm in the course of EDS, as there are not many case reports, not mentioning larger studies covering this issue. 6,18 The treatment outcome in two of three of our patients was only partial improvement. Therefore, the question remains, whether urgent interventional procedure (stent implantation) would improve the outcome.…”

Spontaneous Dissection of the Carotid and Vertebral Arteries: the 10-year UCSD Experience

“…Several case reports and single patient series suggest that carotid stenting may be safe in the setting of SCD. [19][20][21] The patient in this series who underwent carotid stent placement suffered from recurrent symptomatic bilateral carotid dissection while on anticoagulation. (Fig.…”

Asymptomatic bilateral common iliac artery dissections in previously undiagnosed vascular Ehlers-Danlos syndrome

“…Multiple case reports underline the importance of consideration of underlying collagen vascular disease in young patients with unexplained vascular anomalies 15. Arterial complications (including dissection of the abdominal/thoracic aortic, coronary, carotid, subclavian, vertebral, cervical, renal and iliac arteries) have been reported in patients with already diagnosed or previously undiagnosed vEDS 15–23. Often further review of family history will reveal a history of arterial dissections or sudden death in family members24 although notably, there can be significant phenotypic variance in disease presentation in family members.…”