Successful salvage of the left pulmonary artery in a neonate with isolated unilateral absence of the pulmonary artery

Kawada, Kazuo; Saiki, Hiroshi; Kemmochi, Manabu; Kuwata, Seiko; Takanashi, Manabu; Miyaji, Kagami; Senzaki, Hideaki

doi:10.1016/j.jccase.2019.12.004

Cited by 3 publications

(3 citation statements)

References 7 publications

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“…Yang [20] has proposed a new treatment plan. Kawada [21] has recorded the successful diagnosis and treatment of UAPA patients. Wang [22] has analyzed the clinical features of UAPA and confirmed the diagnostic significance of ultrasound.…”

Section: Discussionmentioning

confidence: 99%

Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Tian¹,

Zheng²

2021

Reviews in Cardiovascular Medicine

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The unilateral absence of pulmonary artery (UAPA) is a rare congenital cardiovascular malformation, which is asymptomatic and easy to be ignored in early stage. A large number of complications may occur in the later stage. Therefore, early diagnosis and treatment is of great significance. The imaging data of 49 patients with UAPA discovered and confirmed clinically by the echocardiography in our hospital are analyzed. The results show that left pulmonary artery absence is more common (55%) and most of them are associated with other cardiovascular malformations (92%). Atrial septal defect and patent foramen ovale were most common in 56%. In which the absence of isolated pulmonary artery was 8% (4/49), and the absence of right pulmonary artery was 75% (3/4). Especially in the patients with tetralogy of Fallot, 77% (5/9) of them miss the diagnosis of UAPA. This suggests that doctors and sonographers should pay attention to the development of pulmonary artery bifurcation and left and right branches in multi-section, and strengthen the scanning of short axis section of high large artery.

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Section: Discussionmentioning

confidence: 99%

Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Tian¹,

Zheng²

2021

Reviews in Cardiovascular Medicine

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“…Patients diagnosed with "absent pulmonary arteries" rather have disconnected pulmonary arteries, which are frequently fed from an aberrant arterial duct arising from the origin of the innominate artery [1,2]. In all our patients, the initial diagnosis was absence of one of the pulmonary arteries.…”

Section: Discussionmentioning

confidence: 71%

“…Disconnected pulmonary arteries are frequently misdiagnosed as "absent" [1]. Frequently these are initially fed by an aberrant ductus from the origin of the innominate artery, and become disconnected once the ductus closes [2].…”

Section: Introductionmentioning

confidence: 99%

“Absent” unilateral pulmonary arteries aren't absent, but disconnected. Review of the current literature based on 4 cases

Krasemann¹,

Dalinghaus²,

Beynum³

et al. 2022

Rev. Cardiovasc. Med.

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Background: Disconnected unilateral pulmonary arteries are frequently misdiagnosed as "absent". They typically arise from the base of the innominate artery and are fed by an aberrant arterial duct. If diagnosed early enough, they can be reconnected with catheter techniques even after closure of this aberrant duct. Consecutive surgical anatomical correction at a later stage is possible. Methods: Four cases illustrate the anatomical findings on computed tomography and angiography, all show an outpouching at the base of the brachiocephalic artery. Results: The therapeutic approach consisted of stenting of the aberrant ductus and consecutive surgery. In the oldest patient, 13 years, such an approach was impossible. Conclusion: If identified early in life, disconnected pulmonary arteries can be recruited with catheter techniques, and reconnected surgically at a later stage. It is not yet known if this approach prevents pulmonary damage, which is frequently seen in older untreated patients.

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Analysis of Ultrasonic Features Based on Absence of Pulmonary Artery

Tian

Minjuan

2021

j med imaging hlth inform

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According to clinical features and ultrasonic imaging features of patients with absence of pulmonary artery, it is necessary to analyze ultrasonic imaging features of absence of pulmonary artery to provide clinical basis for improving the diagnostic value and prognosis. The data and color Doppler echocardiography of 45 patients with absence of pulmonary artery are collected, who are confirmed by cardiac catheterization, CTA and operation, and the clinical features and ultrasonic imaging features are studied. The research results show that 57% of the patients have left absence of pulmonary artery and 91% of them have other cardiovascular malformations, where ASD/PFO is the most common, PDA and VSD are the second. Patients with UAPA have changes of pulmonary artery, the incidence of pulmonary artery abnormalities in multiple malformations, changes of ASD/PFO, PDA and VSD are mainly pulmonary hypertension. The ejection fraction of patients with UAPA is normal. The main manifestation of pulmonary hypertension is the increase of right cardiac volume load, and the main manifestation of pulmonary stenosis is the increase of collateral circulation. Pulmonary hypertension and its associated cardiovascular malformations may be related to the prognosis of patients. Ultrasound doctors should understand such diseases to improve the diagnosis rate and the prognosis.

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Successful salvage of the left pulmonary artery in a neonate with isolated unilateral absence of the pulmonary artery

Cited by 3 publications

References 7 publications

Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Unilateral absence of pulmonary artery analysis based on echocardiographic feature

“Absent” unilateral pulmonary arteries aren't absent, but disconnected. Review of the current literature based on 4 cases

Analysis of Ultrasonic Features Based on Absence of Pulmonary Artery

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