Cor triatriatum dexter is a rare congenital heart anomaly where the right atrium is divided into two chambers by a membrane. We report a lady who present to us with orthopnea,engorged pulsatile neck veins, pulsatile enlarged liver and bilateral pedal edema. A diagnosis of multivalvular rheumatic heart disease (RHD) was made clinically. Echocardiography showed mitral stenosis (MS) with aortic regurgitation (AR) with tricuspid regurgitation (TR) with cortriatriatum dexter.
Key Messages:Usually cortriatriatum dexter is associated with other congenital diseases like atrial septal defect (ASD),partial anomalous pulmonary venous connections (PAPVC) etc. Here it is associated with RHD masqueriding as tricuspid stenosis, hence very rare and worth reporting.