Successful Coronary Artery Bypass Grafting in a Patient With Uncontrolled Scleromyxedema

Abstract

Scleromyxedema is a rare disorder characterized by diffuse cutaneous and systemic mucinosis with paraproteinemia. Affected patients usually develop numerous waxy, firm papules and plaques as a result of subcutaneous mucin deposition and fibrosis. Systemic manifestations may involve the cardiovascular, gastrointestinal, pulmonary, musculoskeletal, renal, or nervous systems and are known to lead to significant morbidity and mortality if left untreated. As the skin of these patients can be heavily infiltrated with mucin and fibrosis, it is unknown if scleromyxedema affects wound healing. Additionally, owing to the rarity of the disorder, there is very little data regarding surgical outcomes in these patients and their optimal management in the pre-and post-surgical setting. Herein, we report a case of a patient who underwent elective coronary artery bypass grafting (CABG) while in active relapse of his scleromyxedema; he suffered no pre-or post-operative complications and his surgical incision site healed well without any intervention.