Sturge-Weber syndrome with bilateral intracranial calcification.

Boltshauser, Eugen; Wilson, John; Hoare, R. D.

doi:10.1136/jnnp.39.5.429

Cited by 66 publications

(30 citation statements)

References 10 publications

(1 reference statement)

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“…This has now become the diagnostic test in Sturge-Weber syndrome [2,6,14]. In infancy it shows calcification and atrophy on the involved side at a time when skull X-rays are normal.…”

Section: Computed Tomographic Scanmentioning

confidence: 99%

See 1 more Smart Citation

Hemispherectomy for Sturge-Weber Syndrome

Hoffman¹,

Hendrick²,

Dennis³

et al. 1979

Pediatr Neurosurg

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Patients with Sturge-Weber disease who have the onset of seizures in infancy invariably face a progressively downhill course which leaves them severely hemiplegic, demented and usually institutionalized because of uncontrolled seizures. During the past 12 years, we have carried out 6 hemispherectomies in infants under 1 year of age who presented with seizures and Sturge-Weber disease. The results have been gratifying. Seizures have stopped, hemipareses have been minimal and intellectual development has been good.

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“…This has now become the diagnostic test in Sturge-Weber syndrome [2,6,14]. In infancy it shows calcification and atrophy on the involved side at a time when skull X-rays are normal.…”

Section: Computed Tomographic Scanmentioning

confidence: 99%

“…[2] showed that one-third of all patients with SturgeWeber syndrome have bilateral port-wine nevi but only 15% have involve ment of both cerebral hemispheres.…”

mentioning

confidence: 99%

Hemispherectomy for Sturge-Weber Syndrome

Hoffman¹,

Hendrick²,

Dennis³

et al. 1979

Pediatr Neurosurg

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show abstract

“…Occurrence of bilateral intra cranial calcification is less common, accounting for 17% of reported cases in the literature [4], Also incomplete or atypical cases of this syndrome have been described [3,7,8,15,18], and there is no reason why these should be excluded by definition from the Sturge-Weber syndrome when the basic pathology (namely, leptomeningeal angiomatosis) is present.…”

Section: Introductionmentioning

confidence: 99%

Sturge-Weber Syndrome without Port-Wine Facial Nevus

Ambrosetto

Michelucci³

et al. 1983

Pediatr Neurosurg

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2 cases of Sturge-Weber syndrome without facial nevus are reported. The patients presented different forms of epilepsy. The diagnosis was made by computed tomography (CT) which showed typical intracranial calcifications in both occipital regions. The problems concerning the atypical and incomplete forms of the syndrome are briefly discussed. The importance of CT as a diagnostic procedure for this disease is emphasized.

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“…therefore, the area which could be ablated surgically. Typically the posterior parietal and occipital lobes are involved but isolated frontal [12] and bilateral cortical involvement can be appreciated in up to 15% of patients [4], When bilateral involvement is present, seizures occur at an earlier age and are significantly more difficult to control [2]. As a result, mental retardation appears more profound in patients with bilateral cortical involvement.…”

Section: Discussionmentioning

confidence: 99%

The Natural History of Patients with the Sturge-Weber Syndrome

Oakes

1992

Pediatr Neurosurg

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Sturge-Weber syndrome with bilateral intracranial calcification.

Cited by 66 publications

References 10 publications

Hemispherectomy for Sturge-Weber Syndrome

Hemispherectomy for Sturge-Weber Syndrome

Sturge-Weber Syndrome without Port-Wine Facial Nevus

The Natural History of Patients with the Sturge-Weber Syndrome

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