Steroid-responsive pyoderma gangrenosum with vulvar and pulmonary involvement

Non‐Infective Cutaneous Conditions of the Vulva

“…There have been reports of its association with Behçet's syndrome (Lee & Barnetson 1996) and myeloproliferative disorders. There may be an association or overlap with pyoderma gangrenosum (Lebbe et al 1992) and both conditions have occurred together in myeloproliferative disease and may be part of a continuum (Caughman et al 1983, Kuroda et al 1995.…”

Pyoderma Gangrenosum Presenting with Pulmonary Cavitary Lesions

“…Twenty four patients with neutrophilic dermatoses who had culture negative pulmonary lesions were reported in literature (5-8) Cavitery pulmonary lesions were reported in only two cases (4,5). Pulmonary lesions usually exists concurrent with skin lesions or later but in our case, pulmonary lesions developed before skin lesions.…”

“…Lesions are often limited to the skin, but sterile neutrophilic infiltration can occur in lung, heart, central nervous system, joints, gastrointestinal tract and eyes as well (3). So far, only two cases presenting with cavitary lesions has been reported in the literature (4,5).…”

Violaceous-Rimmed Ulcers

“…The ulcerative form occurs primarily in the extremities or lower trunk (2, 11); however, it has been reported in the vulva, the penis, the breasts, and the head and neck region (12)(13)(14). The lower limbs are involved in >70% of patients, and the lesions may arise either by themselves or in response to minor trauma, insect bites, or surgical procedures (11).…”