Spontaneous long-term survival in single ventricle with pulmonary hypertension

Multiple miscarriages in a female patient with two-chambered heart and situs inversus totalis: A case report

“…Consistent with Blackford’s study[ 11 ], the findings of familial single ventricular patients[ 9 ] and a long-term follow-up study of a 61-year-old patient with single ventricle[ 12 ] support that pulmonary stenosis might be the main reason for longer survival of single ventricular patients. In the current case, pulmonary subvalvular stenosis was present, and pulmonary vascular resistance was normal, with no significant pulmonary hypertension.…”

Long-term survival of a patient with single atrium and single ventricular heart: a case report

“…However, rarely some patients live almost a normal life without any surgical interventions due to a balanced native hemodynamic status. Only around 10 cases have been reported worldwide who survived into late adulthood; age up to 62 years in one and up to 50 years in the rest [3]. We did not find any reports from Sri Lanka of long survival of such patients.…”

An adult female patient with single atrium and single ventricle undergoing appendectomy: A case report

“…Due to the disturbance of the homeostasis of their hemodynamic state, few patients can live an almost normal life without any surgical intervention. Only about 10 cases worldwide have been reported for patients with single ventricle surviving to late adulthood, one of them up to 62 years of age and the others up to 50 years of age (12). Survival to adulthood in patients with a single ventricle combined with a single atrium is even rarer, with only a very few cases reported so far (13,14).…”