Spontaeous capsular ruptures in alport syndrome

Bilateral spontaneous anterior lens capsule ruptures in a child: A rare presentation of Alport syndrome

“…To the best of our knowledge only fourteen cases of anterior lens capsule rupture in AS have been reported in the past fifty years (see Table 1 ). Although a few of these cases went on to develop subsequent spontaneous anterior lens capsule rupture in the fellow eye, 9 bilateral spontaneous ruptures as the presenting feature of AS has not been described before.…”

Femtosecond Laser-Assisted Cataract Surgery in Alport Syndrome with Anterior Lenticonus

“…Earlier studies recommended performing continuous curvilinear capsulorhexis (CCC) after the cortical lens matter was aspirated, or to start it in the midperiphery, rather than a conventional CCC, which is initiated in the center of the capsule, which is thin and fragile at the poles (20, 21). A requirement for gentle but thorough hydrodissection from several sites is reported by several authors to ensure lens nucleus rotation well within the capsular bag, and extreme caution is needed when there are associated posterior subcapsular opacities or posterior lenticonus (5, 9, 19, 20). Satish et al (20) also found it important not to polish the posterior capsule as it can also be thinner than in normal patients.…”

Phacoemulsification and intraocular lens implantation in Alport syndrome with anterior lenticonus

“…Our findings are comparable to those in the reports by John et al 7 and Sukhija et al 8 In two of the earlier studies, a CCC was performed after the cortical lens matter was aspirated, as in a 2-stage CCC. 10,14 We performed a CCC starting in the midperiphery rather than a conventional CCC, which is initiated in the center of the capsule. This step is important because it avoids inadvertent spontaneous rupture of the lens capsule, which is thin and fragile in Alport syndrome.…”