Spinal Extradural Meningeal Cyst in Klippel-Trenaunay Syndrome

Choi, Kyung-Chul; Ahn, Sung Tae; Shin, Yong Hawn; Lee, Sang-Ho

doi:10.3340/jkns.2011.49.5.299

Cited by 4 publications

(4 citation statements)

References 21 publications

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“…Spinal extradural cysts by itself are exceedingly uncommon in pediatric patients, so it wasn’t surprising that to this day and with an in-depth search of various databases, we’ve only come across two reported cases of spinal extradural cysts in patients with KTS 12 , 13 . Therefore, our documentation of a thoraco-lumbar extradural cyst in a 15-year-old patient with KTS syndrome which was managed at Tishreen University Hospital is valuable input to medical literature.…”

Section: Introductionmentioning

confidence: 99%

Surgical management of a thoraco-lumbar extradural cyst in a pediatric patient with Klippel–Trenaunay syndrome: a case report

Zaino,

Ibrahem,

Joha

et al. 2024

Annals of Medicine &Amp; Surgery

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Introduction and Importance: Klippel-Trenaunay Syndrome (KTS) is a congenital disorder characterized by the abnormal development of blood vessels, soft tissues, bones, and the lymphatic system. The syndrome is rare, with few cases reported worldwide, especially those describing an association between KTS and spinal extradural meningeal cysts (SEMC). This report highlights a rare case of a pediatric patient with Klippel-Trenaunay Syndrome who underwent successful surgical decompression of a thoracolumbar extradural cyst, highlighting the importance of reevaluating surgical interventions in KTS patients. Case Presentation: A 15-year-old girl diagnosed with Klippel-Trenaunay Syndrome four days postnatally, was referred to our clinic due to chronic back pain and spastic paraparesis. These symptoms were attributed to a compressive extradural thoracolumbar cyst. Diagnostic evaluations confirmed the presence of the cyst, leading to the decision to proceed with surgical intervention. Clinical Discussion: The surgical approach involved a laminoplasty at T11-T12-L1, resulting in the total removal of the cystic lesion. The patient exhibited a complete resolution of symptoms post-operatively, with no significant complications reported during the surgery. Conclusion: With this case, we question the fear of surgical intervention in Klippel-Trenaunay Syndrome patients, which is often avoided due to concerns of high-risk complications like excessive bleeding or poor wound healing, and hint at a possible association between KTS and Extradural Meningeal Cysts.

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Section: Introductionmentioning

confidence: 99%

Surgical management of a thoraco-lumbar extradural cyst in a pediatric patient with Klippel–Trenaunay syndrome: a case report

Zaino,

Ibrahem,

Joha

et al. 2024

Annals of Medicine &Amp; Surgery

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“…Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder characterized by the triad of capillary malformations such as port wine stains, soft tissue or bone hypertrophy involving limb asymmetry, and venous malformations or varicose veins [1][2][3][4][5]. Complications of delayed diagnosis of KTS include thrombophlebitis, pulmonary embolism, stasis dermatitis, cutaneous ulcerations, and bleeding [6].…”

Section: Introductionmentioning

confidence: 99%

Klippel-Trenauney syndrome with axillary hyperhidrosis

Lim

Rosmarin²,

Klement³

et al. 2017

Dermatology Online Journal

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“…Klippel–Trenaunay syndrome (KTS) is a rare congenital disorder with a triad of vascular malformations, for example port wine stains, venous varicosities, and bony or soft tissue hypertrophy involving an extremity . Early diagnosis is important to avoid complications, such as thrombophlebitis, pulmonary embolism, stasis dermatitis, cutaneous ulcerations, and bleeding .…”

Section: Introductionmentioning

confidence: 99%